HEREDITER SFEROSITOZ
Abstract
Klinigimizde 1980-1990 yillari arasinda izledigimiz 22 herediter
sferositozisli hasta degerlendirilmistir. Hastalarimizin 11’'i erkek, 11’i
kizdi, Fizik bulgu olarak hepsinde degisik agirlikta anemi, splenomegali, % 38 inde ikter vardi. Ayrica 3°tinde neonatal ikter, 3 inde aplastik kriz, ikisinde kolelithiazis ve birinde hemoglobiniiri vardi. Hastalarimizin 14’ne splenektomi yapuldi. Splenektomi yas ortalamési
8.36 + 4.13 tu. Splenektomi sonrasi izlenen hastalarimizda klinik ve
hematolojik sorun kalmamisti.
Keywords
References
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