Incomplet Prune - Belly Syndrome
Abstract
An eight year old boy was admitted to our clinic because of abdominal distention. He had partial absence of abdominal wall musculature, bilateral hydronephrosis and urethral obstruction. No other abnormalities were identified. Cryptorchidism was not present. Because of this and partial absence of abdominal wall musculature our patient was accepted as incomplet PBS.
Keywords
References
- 1. Adeyokonnu AA, Famulusi JB : Prune Belly Syndrome in two siblings and a first cousin, Am J Dis Child 136 : 23-25, 1982.
- 2. Duckett JW : The Prune-Belly Syndrome from clinical Pediatric Urology Ed. by Kelalis PP, King LR. WB Saunders Comp Philadelphia-London-Toronto 1976, p : 615-635.
- 3, Geary DF, MacLusky IB, Churchill BM, McLorie G : A broader spectrum of abnormalities in the Prune-Belly Syndrome. J Urol 135 : 324-326, 1986.
- 4, Gonzales R, Michael A : Prune-Belly Syndrome from Nelson Textbook of Pediatrics. 13th ed. Ed by Behrman RE, Vaughan VC. WB Saunders Comp. Philadelphia-London Toronto 1987, P. 1157.
- 5. Meizner I, Bar-Ziv J: Prenatal ultrasonic diagnosis of anterior abdominal wall defects. Eur J Obstet Gynecol Reprod Biol 22 : 217-224, 1986.
- 6. Moerman P, Fryns JP, Goddeeris P, Lauweryns JM : Pathogenesis of the Prune - Belly Syndrome : A functional urethral obstruction caused by prostatic hypoplasia. Pediatrics 73 : 470-474, 1984.7. Nakayama DK, Harrison MR, Chinn DH, Lorimier AA : The pathogenesis of Prune - Belly. AJDC 138 : 834-836, 1984.
- 8. Pagon RA, Smith DW, Shepard TH : Urethral obstruction malformation complex : A cause of abdominal muscle deficiency and the «Prune-Belly» J Pediatr 94 : 900-906, 1979.
- 9. Woodhouse CRJ, Ransley PG, Innes-Williams D : Prune - Belly Syndrome report of 47 cases. Arch Dis Child 57 : 856-859, 1982.