Renal Amyloıd- Ourstııcasrı A And Deafness

Year 1979, Volume: 32 Issue: 3, 415 - 418, 01.01.1980

Atilla İlhan Özdemir

https://izlik.org/JA84AU89GM

Abstract

A 48 - year -old patient with progressive bilateral perceptive deafness, bouts ol fever, chronic urticaria, pes cavus and rena! amyloidosis is derseribed. The case was characterized by long duration (14 years) with initial involment of the kidneys and subseguent development of deafness. This represents the third (sporadic) instance of the clinical syndrome initialliy described by Muckle and Wells.

Keywords

Chronic urticaria , Renal amyloidosis , Progressive hearing loss , Muckle-Wells syndrome , Autoinflammatory syndrome

Ethical Statement

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Supporting Institution

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Thanks

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BÖBREK AMİLOİDOZİSİ, ÜRTİKER VE SAĞIRLIK Bir olgu ve literatürün Gözden Geçirilmesi

https://izlik.org/JA84AU89GM

Abstract

ift yanlı perseptif sağırlık, ateş nöbetleri, kronik ürtiker, pes kavus ve böbrek amiloidozisi gösteren 48 yaşında bir erkek hasta takdim edildi. Bu olgu son görüldüğünde 14 yıldır yaşıyordu. Önce böbrek bozukluğu, sonradan sağırlık ortaya çıkmıştır. Bu, Muckle ve Wells'in ileri sürdüğü sendromun belirtilerini gösteren üçüncü sporadik olguyu oluşturmaktadır.

Keywords

Muckle-Wells sendromu , Progresif işitme kaybı , Renal amiloidoz , Kronik ürtiker , Otoinflamatuar sendrom

References

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