Çocukta Wilson Sirozu Ve Çinko Tedavisi

Year 1987, Volume: 40 Issue: 2, 131 - 140, 30.06.1987

Gülsan Yavuz

https://izlik.org/JA45RU58LN

Abstract

Hemolitik anemi semptomlarıyla muayene edilen ve Wilson hastalığı tanısı konulan 9 yaşında bir olgu sunulmaktadır.

Anemi, sarılık, splenomegali, retikülositoz ve kemik iliğinde eritroid hiperaktivite saptanan hastaya demir eksikliği nedeni araştırılmış, ultrasonografide karaciğerde sirotik değişiklikler ve portal vende ileri derecede genişleme saptanmıştır.

Çocukluk çağında siroz nedenleri arasında Wilson hastalığı da düşünülerek yapılan tetkikler sonucunda Wilson hastalığı tanısı doğrulanmıştır. Çinko tedavisine başlanan hasta ancak kısa bir süre takip edilebilmiştir. Ailenin ifadesine göre hasta ani gelişen anemi ve sarılık nedeniyle çok kısa sürede hayatını kaybetmiştir.

Keywords

ÇOCUKTA WİLSON SİROZU VE ÇİNKO TEDAVİSİ , çinko , tedavi

Wilson Cirrhosis in Children and Zinc Treatment

https://izlik.org/JA45RU58LN

Abstract

A 9-year-old case, who was examined with hemolytic anemia symptoms and diagnosed with Wilson's disease, is presented.The patient, who showed anemia, jaundice, splenomegaly, reticulocytosis, and erythroid hyperactivity in the bone marrow, was investigated for the cause of iron deficiency, and ultrasonography revealed cirrhotic changes in the liver and advanced dilatation in the portal vein.As a result of the examinations conducted considering Wilson's disease among the causes of cirrhosis in childhood, the diagnosis of Wilson's disease was confirmed. The patient, who was started on zinc treatment, could only be monitored for a short time. According to the family's statement, the patient died in a very short time due to sudden anemia and jaundice.

Keywords

WILSON CIRRHOSIS IN CHILDREN AND ZINC TREATMENT , zınc , treatment

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