Abstract
Male pseudohermaphroditism is a rare intersex condition wherein individuals possess male (XY) chromosomes and testes but exhibit variable external genitalia and, in some cases, Müllerian structures such as a uterus. In this report, we present a case of a 26-year-old man who was admitted for cryptorchidism with both testes located in the right hemiscrotum. During surgical exploration, in addition to two distinct testicular structures, a uterus and fallopian tubes were identified and subsequently removed. Karyotype analysis confirmed a 46,XY male genotype. Histopathology revealed hypoplastic testes and Müllerian remnants. The patient underwent successful orchidopexy with no postoperative complications. This case illustrates an exceedingly rare form of male pseudohermaphroditism falling outside traditional classification schemes, highlighting the need for individualized surgical and diagnostic approaches.
References
- 1. Smith DR. *General Urology*. 1975; pp. 436–443. 2. Walsh PL, Migeon CJ. The phenotypic expression of selective disorders of male sexual differentiation. *J Urol*. 1978;119(5):627–630. 3. Glenn JF. *Urologic Surgery*. 1977; pp. 33–34. 4. Jones HW Jr., Ferguson-Smith MA, Heller RH. Pathologic and cytogenetic findings in true hermaphroditism. *Obstet Gynecol*. 1965;25(4):435–447. 5. Pluefer OH, Schmidt DM, Harrod CS. True hermaphroditism with unambiguous male phenotype. *J Urol*. 1974;112(3):406–408. 6. Denton CJC. A case of polyorchidism with intersex. *J Urol*. 7. Lapides J. *Fundamentals of Urology*. 1976; pp. 244–248. 8. Dubin L, Walsh PC, Amelan RD. *Male Infertility*. 1977; pp. 48–50.
Abstract
Erkek psödohermafroditizmi, erkek (XY) kromozom yapısına ve testislere sahip bireylerde dış genital yapının değişken görünümler sergilediği, bazen Müller kanalına ait uterus gibi yapılarla birlikte görülebilen nadir bir interseks durumdur. Bu bildiride, her iki testisi sağ skrotumda lokalize olarak bulunan 26 yaşında bir erkek hasta sunulmuştur. Cerrahi eksplorasyon sırasında testislerin yanı sıra uterus ve tuba uterinalar saptanarak eksize edilmiştir. Karyotip 46,XY olup erkek olarak doğrulanmıştır. Histopatolojik inceleme testislerde hipospermatogenez ve Müller kalıntılarını ortaya koymuştur. Orkidopeksi sonrası postoperatif komplikasyon gelişmemiştir. Vaka, klasik sınıflandırmalara uymayan nadir bir erkek psödohermafroditizm formunu temsil etmekte olup tanı ve tedavide bireyselleştirilmiş yaklaşım gerekliliğini vurgulamaktadır.
References
- 1. Smith DR. *General Urology*. 1975; pp. 436–443. 2. Walsh PL, Migeon CJ. The phenotypic expression of selective disorders of male sexual differentiation. *J Urol*. 1978;119(5):627–630. 3. Glenn JF. *Urologic Surgery*. 1977; pp. 33–34. 4. Jones HW Jr., Ferguson-Smith MA, Heller RH. Pathologic and cytogenetic findings in true hermaphroditism. *Obstet Gynecol*. 1965;25(4):435–447. 5. Pluefer OH, Schmidt DM, Harrod CS. True hermaphroditism with unambiguous male phenotype. *J Urol*. 1974;112(3):406–408. 6. Denton CJC. A case of polyorchidism with intersex. *J Urol*. 7. Lapides J. *Fundamentals of Urology*. 1976; pp. 244–248. 8. Dubin L, Walsh PC, Amelan RD. *Male Infertility*. 1977; pp. 48–50.
Details
| Primary Language | English |
|---|---|
| Subjects | Urology |
| Journal Section | Systematic Reviews and Meta Analysis |
| Authors | |
| Publication Date | December 31, 1978 |
| IZ | https://izlik.org/JA74XP72ZR |
| Published in Issue | Year 1978 Volume: 31 Issue: 4 |