Türkiye'de Ailevi Akdeniz Ateşi

Cavit Sökmen

TR EN

Türkiye'de Ailevi Akdeniz Ateşi

Abstract

From January 1958 through June 1969, 77 Turkish patients with clinical features of familial Mediterranean fever (FMF)—paroxysmal fever attacks, serositis (peritonitis, pleuritis), arthralgias, and abdominal pain—were identified at Ankara University’s Second Department of Internal Medicine. Ages at onset ranged from 1 to 48 years (mean 28), with 75% presenting before age 20. Recurrent attacks lasted 1–6 days at irregular intervals. Laboratory findings included leukocytosis, elevated sedimentation rate, and proteinuria in 62% of cases; renal biopsy in 45 of 48 proteinuric patients confirmed amyloidosis in 57%. A review of the Turkish and international literature added 49 previously reported Turkish cases, bringing the total to 126. These data demonstrate that FMF is a significant hereditary serositis syndrome among Turks, with amyloid nephropathy as its most serious complication.

Keywords

familial Mediterranean fever, FMF, amyloidosis, hereditary serositis

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Details

Primary Language

English

Subjects

Internal Diseases

Journal Section

Research Article

Authors

Cavit Sökmen This is me
Türkiye

Publication Date

August 31, 1970

Submission Date

July 1, 1970

Acceptance Date

August 31, 1970

Published in Issue

Year 1970 Volume: 23 Number: 4

IZ

https://izlik.org/JA59TE39CS

APA

Sökmen, C. (1970). Türkiye’de Ailevi Akdeniz Ateşi. Ankara Üniversitesi Tıp Fakültesi Mecmuası, 23(4), 1039-1051. https://izlik.org/JA59TE39CS

AMA

1.Sökmen C. Türkiye’de Ailevi Akdeniz Ateşi. Ankara Üniversitesi Tıp Fakültesi Mecmuası. 1970;23(4):1039-1051. https://izlik.org/JA59TE39CS

Chicago

Sökmen, Cavit. 1970. “Türkiye’de Ailevi Akdeniz Ateşi”. Ankara Üniversitesi Tıp Fakültesi Mecmuası 23 (4): 1039-51. https://izlik.org/JA59TE39CS.

EndNote

Sökmen C (August 1, 1970) Türkiye’de Ailevi Akdeniz Ateşi. Ankara Üniversitesi Tıp Fakültesi Mecmuası 23 4 1039–1051.

IEEE

[1]C. Sökmen, “Türkiye’de Ailevi Akdeniz Ateşi”, Ankara Üniversitesi Tıp Fakültesi Mecmuası, vol. 23, no. 4, pp. 1039–1051, Aug. 1970, [Online]. Available: https://izlik.org/JA59TE39CS

ISNAD

Sökmen, Cavit. “Türkiye’de Ailevi Akdeniz Ateşi”. Ankara Üniversitesi Tıp Fakültesi Mecmuası 23/4 (August 1, 1970): 1039-1051. https://izlik.org/JA59TE39CS.

JAMA

1.Sökmen C. Türkiye’de Ailevi Akdeniz Ateşi. Ankara Üniversitesi Tıp Fakültesi Mecmuası. 1970;23:1039–1051.

MLA

Sökmen, Cavit. “Türkiye’de Ailevi Akdeniz Ateşi”. Ankara Üniversitesi Tıp Fakültesi Mecmuası, vol. 23, no. 4, Aug. 1970, pp. 1039-51, https://izlik.org/JA59TE39CS.

Vancouver

1.Cavit Sökmen. Türkiye’de Ailevi Akdeniz Ateşi. Ankara Üniversitesi Tıp Fakültesi Mecmuası [Internet]. 1970 Aug. 1;23(4):1039-51. Available from: https://izlik.org/JA59TE39CS

Türkiye'de Ailevi Akdeniz Ateşi

Familial Mediterranean Fever in Türkiye

Abstract

Türkiye'de Ailevi Akdeniz Ateşi

Abstract

Keywords

References

Details

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Subjects

Journal Section

Authors

Publication Date

Submission Date

Acceptance Date

Published in Issue

IZ

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