Dubin-Johnson Syndrome Seen in 2 Siblings Histopathological Examination
Abstract
Ages 10 and 12 with Duhin-Johnson Syndrome Clinical, laboratory and histopathological findings of the liver in two sisters has been examined. Clinically, jaundice, fatigue, loss of appetite, occasional abdominal pain, laboratory examination hyperbilirubinemia, increase in the amount of direct bilirubin in the serum, bilirubinuria, light color of the stool, opaque substance administered Inability to see the gallbladder in cholecystography, liver biopsy In the histopathological examination of the material, liver Coarse granular dark brown-black color in parenchyma cells It was determined that a pigment accumulated. Other pathological findings not found.
Keywords
Dubin-Johnson Syndrome, Chronic jaundice, Hyperbilirubinemia
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