Stuart-Prower Factor (Factor X) Deficiency

Year 1967, Volume: 20 Issue: 4, 653 - 659, 31.12.1967

Ayhan Okçuoğlu Çavdar

https://izlik.org/JA67BD79AK

Abstract

Congenital Factor X or Stuart Prower deficiency, a rare coagulation defect has been presented in a 2,5 years old girl. Clinical, laboratory and genetic features of the disease have been discussed. This is the second reported case of congenital Stuart-Prower deficiency in Turkey.

Keywords

Factor X Deficiency , Stuart-Prower Factor , Congenital Coagulation Defect

Ethical Statement

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Supporting Institution

Ankara University, Faculty of Medicine, Department of Pediatrics and Child Health

Project Number

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Thanks

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Stuart-Prower (Faktör X) Eksikliği

https://izlik.org/JA67BD79AK

Abstract

Nadir konjenital koagülasyon defektlerinden biri olan Faktör X veya Stuart Prower faktörü eksikliği 2,5 yaşında bir kız çocuğunda takdim edildi. Hastalığın klinik, laboratuar ve genetik hususiyetleri münakaşa edildi. Vak'a Türkiye'den bildirilen 2. ci Stuart-Prower Faktörü eksikliği olarak dikkati çekti.

Keywords

Faktör X Eksikliği , Stuart-Prower Faktörü , Konjenital Koagülasyon Defekti

Ethical Statement

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Supporting Institution

A. Ü. Tıp Fakültesi Çocuk Hastalıkları ve Sağlığı Kliniği

Project Number

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Thanks

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References

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• 2- GASTON, W.: Blood clotting Factors I, II. New England J. of Medicine 270, 236, 1964.
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• 4- LEACHLER, E., WEBSTER, W. P, ROBERTS, H. R. and PENICK G. D.: The inheteritance of stuart Disease: Investigation of a family with Factor X deficieny Am. J. Med. Sci. 249, 291, 1965.
• 5- TÜMAY, S. B., M, BERKARDA, B. and DERMAN, H.: Congenital stuart factor deficiency. New Ist. Cont. Clin. Science. 6 50, 1963
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• 9- YATZİDİS, K., and RICHET,, J.: Activite de certaines proteines de la coagulation dans le plasma et les urines au cours du syndrome nephrotique Rev. Franc. Etudes clin. Biol. 2: 717, 1957.
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