Stuart-Prower (Faktör X) Eksikliği

Year 1967, Volume: 20 Issue: 4, 653 - 659, 31.12.1967

Ayhan Okçuoğlu Çavdar

Abstract

Nadir konjenital koagülasyon defektlerinden biri olan Faktör X veya Stuart Prower faktörü eksikliği 2,5 yaşında bir kız çocuğunda takdim edildi. Hastalığın klinik, laboratuar ve genetik hususiyetleri münakaşa edildi. Vak'a Türkiye'den bildirilen 2. ci Stuart-Prower Faktörü eksikliği olarak dikkati çekti.

Keywords

Faktör X Eksikliği, Stuart-Prower Faktörü, Konjenital Koagülasyon Defekti

Ethical Statement

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Supporting Institution

A. Ü. Tıp Fakültesi Çocuk Hastalıkları ve Sağlığı Kliniği

Project Number

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Thanks

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Stuart-Prower Factor (Factor X) Deficiency

Abstract

Congenital Factor X or Stuart Prower deficiency, a rare coagulation defect has been presented in a 2,5 years old girl. Clinical, laboratory and genetic features of the disease have been discussed. This is the second reported case of congenital Stuart-Prower deficiency in Turkey.

Keywords

Factor X Deficiency, Stuart-Prower Factor, Congenital Coagulation Defect

Ethical Statement

-

Supporting Institution

Ankara University, Faculty of Medicine, Department of Pediatrics and Child Health

Project Number

-

Thanks

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References

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