A case of primary Ewing sarcoma presenting with a vulvar mass

Year 2023, Volume: 3 Issue: 2, 52 - 55, 30.12.2023

Ezgi Ada Kaya , Ayşe Özkan

Abstract

Ewing sarcoma/Primitive Neuroectodermal Tumor (ES/PNET) is a high-grade malignant neoplasm that often arises from the skeletal system. Primary extraosseous ES/PNET is a condition that rarely affects the female genital system. Few cases of primary vulvar and vaginal ES have been published to date. In this article, an 11-year-old case of primary ES, one of the youngest cases in the literature, originating from the labium majus and treated successfully with multidisciplinary treatment, is presented.

Keywords

extraosseous Ewing sarcoma, PNET, vulvar mass

Vulvada kitle ile başvuran primer Ewing sarkom olgusu

Abstract

Ewing sarkomu/Primitif Nöroektodermal tümör (ES/PNET), sıklıkla iskelet sisteminden gelişen, yüksek dereceli malign bir neoplazmdır. Primer ekstraosseöz ES/PNET, kadın genital sistemini nadiren etkileyen bir durumdur. Bugüne kadar az sayıda primer vulvar ve vajinal ES vakası yayınlanmıştır. Bu yazıda, labium majus bölgesinden kaynaklanan ve multidisipliner tedavi ile başarılı bir şekilde tedavi edilen literatürün en genç vakalarından biri olan 11 yaşında bir primer ES olgusu sunulmuştur.

Keywords

ekstraosseöz Ewing sarkom, PNET, vulvar kitle

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