Halsizlik ve iştahsızlık yakınması ile gelen restriktif kardiyomiyopatili bir olgu

Year 2018, , 151 - 155, 27.08.2018

Tülay Demircan , Özgür Kızılca Cüneyt Zihni Bahattin Öncü Mustafa Kır , Nurettin Ünal

https://doi.org/10.5505/deutfd.2018.38233

Abstract

Restriktif kardiyomiyopati (RKMP)
çocukluk çağının nadir görülen kardiyomiyopatilerindendir. Çocukluk çağı
RKMP’lerinin çoğunda altta yatan patoloji bulunamaz ve mortalitesi yüksektir.
Karakteristik morfolojik özelliği ventrikül boyutları normal, ventriküler duvar
kalınlığı normal veya artmış ve biatriyal büyümedir. Konstriktif perikarditle
ayırıcı tanısı önem taşır. Bu yazıda, 2,5 yaşında RKMP’li bir olgu literatür
eşliğinde tartışılmıştır.

Keywords

Restriktif kardiyomiyopati, Konstriktif perikardit, çocuk

A CASE OF RESTRICTIVE CARDIOMYOPATHY IN CHILDHOOD PRESENTING WITH WEAKNESS AND ANOREXIA

Abstract

Restrictive cardiyomyopathy (RCM) is a very
rarely diagnosed cardiyomyopathy in childhood. Most RCM in childhood is
idiopathic with a high mortality. Biatrial enlargement and normal sized
ventricles with normal or increased ventricular wall thickness are the
characteristic morphological features of RCM. The differential diagnosis of
constrictive pericarditis is important. In this article a patient at 2.5 years
of age with RCM is discussed regarding the literature.

Keywords

Restrictive cardiomyopathy, Constrictive pericarditis, child

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