Primer İntestinal Lenfanjiektazi: Diyet tedavisine yanıt veren bir olgu

Yıl 2015, Cilt: 29 Sayı: 1, 45 - 49, 24.03.2016

Ahmet Baştürk

Öz

İntestinal lenfanjiektazi, hipoalbuminemi
bulgusu olan hastalarda çok nadir görülen protein kaybettiren enteropati
nedenidir.
Genellikle çocukluk ve genç erişkin yaşlarda sporadik veya ailesel olarak
ortaya çıkar. Büyüme geriliği ve kronik
ishal yakınması ile başvuran dokuz aylık kız bebekte periferik ödem ve
hipoalbüminemi bulgusu dikkati çekti. Hipoalbuminemi ayırıcı tanısında fekal
alfa 1 antitripsin düzeyi yüksekliği nedeniyle endoskopi ve biyopsi yapıldı.
Endoskopide görünen beyaz plaklar ve biyopsi materyalinin histopatolojik
incelemesinde geniş laktealler saptanarak intestinal lenfanjiektazi tanısı
kondu. Sekonder nedenler dışlandığı için primer intestinal lenfanjiektazi düşünüldü. Hasta proteinden
zengin, düşük yağlı, orta zincirli yağ asitlerinden zengin trigliserid içeren
tedavi amaçlı beslenme düzenlemesine yanıt verdi. 

Anahtar Kelimeler

Lenfanjiektazi, protein kaybettiren enteropati, endoskopi, biyopsi

Kaynakça

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