A CASE WITH WOLFRAM (DIDMOAD) SYNDROME AND ORAL FINDINGS (A CASE REPORT)

Year 2007, Issue: 014, 137 - 140, 17.12.2007

Hasan Hatipoğlu Müjgan Güngör Hatipoğlu Özden Kansu

Abstract

Wolfram Syndrome is an unusual, congenital, multi system disorder. Diabetes mellitus, Diabetes insipidus, optic

atrophy and deafness are most observable symptoms. Neurological, urinary tract and psychiatric disorders are the

other common symptoms. Diabetes mellitus and optic atrophy are usually the first findings.

In this case report we present 20 year old-male patient, that was have Wolfram syndrome. Oral clinical and

radiological findings were presented.

Keywords

Wolfram Syndrome, DIDMOAD, oral findings

WOLFRAM (DIDMOAD) SENDROMU BULUNAN BİR OLGUDAKİ ORAL BULGULAR (OLGU BİLDİRİMİ)

Abstract

Wolfram Sendromu, nadir görülen konjenital, birçok sistemi etkileyebilen sendromdur. Diabetes mellitus,

diabetes insipidus, optik atrofi ve sağırlık ile karakterizedir. Hastalarda nörolojik rahatsızlıklar ile üriner sistem

rahatsızlıkları ve psikolojik rahatsızlıklar da izlenir. Diabetes mellitus ve optik atrofi ilk ortaya çıkan bulgulardır.

Bu olgu raporunda 20 yaşındaki Wolfram sendromlu erkek hastanın klinik ve radyografik ağız bulguları

sunulmaktadır.

Keywords

Wolfram sendromu, DIDMOAD, oral bulgular

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