PARAGANGLIOMA OF THE ORGAN OF ZUCKERKANDL : REPORT OF A CASE

Year 2005, Issue: 008, 245 - 252, 15.07.2005

C. Algın A. Hacıoğlu E. Dündar H. Kiper A. Saral

Abstract

Tumors of the paraganglionic system will arise; these are termed paragangliomas, as they may be both physiologically and histopathologically similar to pheochromocytomas of the adrenal gland. Extra-adrenal paragangliomas make up approximately ten per cent of all paragangliomas, with those occuning in the organ of Zuckerkandl being the most common We describe a case of paraganglioma in a 51-year-old woman with hypertension being present for 32 years. She suffered from abdominal mass, nausea, dizziness, emesis, headache, excessive sweating, palpitations, and back pain. An abdominal mass was diagnosed as a functional extra-abdominal paraganglioma by diagnostic imaging and biochemical tests. The mass was totally excised and her symptoms healed after the operation. Symptoms of tumors of the organ of Zuckerkandl are secondary to synthesis and release of excess catecholamines. This is a rare case of functional paraganglioma arising from the organs of Zuckerkandl with successful surgical removal and amelioration of hypertension.

Keywords

Organ of Zuckerkandl, Paraganglioma

ZUCKERKANDL ORGANI PARAGANGLiOMASI: VAKA TAKDiMi

Abstract

Retroperitoneal paragangliomalar; aorta cevresinde sempatik zincirle birlikte dagilnus olan ozellesrnis noral krest hucrelerinden kaynaklanrnaktadrr. Bu makalede 32 yillik hipertansiyon hikayesi olan 52 yasmda bir bayan hasta paraganglioma vakasi olarak takdim edilmektedir. Hastada kannda kitle, bulanti, kusma, bas agnsi, bas donrnesi, asm terleme, carpmn ve sut agnsr gibi sikayetler mevcuttu. Yapilan radyolojik ve biyokimyasal incelemeler, kanndaki kitlenin aktif fonksiyon gosteren ekstraabdominal bir paraganglioma oldugunu gosterdi. Kitlenin tamarru eksize edildi ve ameliyat sonrasi hastanm sernptomlan normale dondu.

Keywords

Paraganglioma, Zuckerkandl Organı

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