Neuro-Behçet Presenting with Venous Sinus Thrombosis: Case Report

Abstract

Behçet disease is an inflammatory disease of unknown etiology with multisystem involvement. Central nervous system (CNS) involvement is rare, but may sometimes been before the other systems involvements. CNS involvement is seen in 5-15% of the cases. Early diagnosis and treatment is critical in terms of prevent the sequellae. CNS involvement could be the first reason of the patient to consult the hospital in the cases that carry the fundamental criteria for Behçet disease diagnosis, but not diagnosed yet. In this report, we presented a neurobehçet case admitted to hospital due to severe headache and diplopia, and detecting cerebral vein thrombosis resulting from Behçet disease in etiology. We found this case worth to present since the etiological reason forms the treatment in venous sinus thrombosis and our patient was diagnosed neuro-behçet before than the Behçet disease.

Keywords

• Behçet disease,venous sinus thrombosis,headache

Venöz Sinüs Trombozu ile Prezente olan Nörobehçet: Olgu Sunumu

Abstract

Behçet hastalığı etiyolojisi bilinmeyen, multisistem tutulumlu enflamatuar bir hastalıktır. Santral sinir sistemi (SSS) tutulumu nadir olmakla birlikte bazen diğer sistem tutulumlarından önce olabilir. SSS tutulumu vakaların %5-15’inde görülmektedir. Erken teşhis ve tedavi, sekelleri önlemek açısından önemlidir. SSS tutulumu, Behçet hastalığı tanısı için gerekli kriterleri taşıyan, ancak henüz tanı almamış vakalarda hastaneye ilk başvuru nedeni olabilir. Bu yazıda, şiddetli baş ağrısı ve çift görme nedeniyle hastaneye başvuran ve tetkiklerinde serebral venöz sinüs trombozu tesbit edilip etiyolojide Behçet hastalığı çıkan nörobehçet olgumuzu sunduk. Venöz sinüs trombozunda etiyolojik neden tedaviyi şekillendirdiği ve hastamız Behçet hastalığıdan önce nörobehçet tanısı aldığı için sunmaya değer bulduk.

Keywords

• Behçet hastalığı,venöz sinüs trombozu,baş ağrısı

References

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