A Case of Familial Mediterranean Fever Who Was Presented with Acute Coronary Syndrome

Abstract

Familial Mediterranean fever is an autosomal recessive disease manifested by recurrent attacks of peritonitis, plevritis and arthritis, and characterized by clinical, histological and laboratory evidence for localized and systemic inflammation. Systemic inflammation is an important factor in the initiation and development of atherosclerosis. We report here a patient with long-standing FMF who was presented with acute coronary syndrome during the febrile attacks

Keywords

• Familial Mediterranean fever, Acute Coronary Syndrome, Inflammation

Akut Koroner Sendrom ile Prezente Olan Ailesel Akdeniz Ateşi (FMF) Olgusu

Abstract

Ailesel Akdeniz Ateşi (FMF), klinik olarak tekrarlayan peritonit, plevrit ve artrit gibi seröz zar tutulumuyla karakterize, histolojik ve laboratuar bulgularıyla lokalize veya sistemik inflamasyon kanıtları olan, otozomal resesif geçiş gösteren genetik bir hastalıktır. Sistemik inflamasyon, ateroskleroz başlangıcı ve gelişimi açısından önemli bir faktördür. Biz burada uzun süredir FMF tanısıyla tedavi alan bir hastanın, febril atakları esnasında akut koroner sendrom gelişerek semptom verebileceğini gösterdik

Keywords

• Ailesel Akdeniz Ateşi,Akut Koroner sendrom,İnflamasyon

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