A Rare Association; Pulmonary Artery Sling and Mowat-Wilson Syndrome

Year 2013, Volume: 15 Issue: 2, 49 - 51, 01.07.2013

Fatih Köksal Binnetoğlu Naci Topaloğlu Mustafa Tekın Şule Yıdırım Nazan Kaymaz Abdullah Sarıyıldırım

Abstract

Pulmonary artery sling anomaly, where the left pulmonary artery originates from the rightpulmonary artery is a rare type of vascular ring that can cause respiratory difficulties, cough,wheezing, stridor, feeding difficulties and repetitive vomiting due to tracheal and esophagealcompression. We present a 14-year-old patient with dysmorphic facial appearance and mildmental retardation who underwent an echocardiography for murmur and was diagnosed withpulmonary artery sling anomaly

Keywords

Mowat Wilson syndrome, pulmonary artery sling, vascular ring

Nadir Bir Birliktelik; Pulmoner Arter Sling ve Mowat Wilson Sendromu

Abstract

Sol pulmoner arterin sağ pulmoner arterden çıktığı pulmoner sling anomalisi nadir bir vaskülerhalka tipi olup trakeaya ve özafagusa bası yaparak solunum sıkıntısı, öksürük, hırıltı, stridor,beslenme problemleri ve tekrarlayan kusmalara yol açabilir. Bu yazıda dismorfik yüz yapısı,hafif mental retardasyon nedeniyle izlenen ve üfürüm nedeniyle yapılan ekokardiyografidepulmoner arter sling anomalisi saptanan 14 yaşındaki bir olgu sunulmuştur

Keywords

Mowat Wilson Sendromu, pulmoner arter sling, vasküler halka

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