ALVEOLAR RHABDOMYOSARCOMA OF THE HAND: A VERY RARE CASE OF SOFT TISSUE SARCOMA

Year 2014, Volume: 16 Issue: 2, 43 - 45, 01.07.2014

Bilgehan Tosun Tuncay Baran Hakan Sarman

Abstract

Soft tissue sarcomas of extremities are very rare and generally have a bad prognosis.Rhabdomyosarcomas are soft tissue sarcomas that, while extremely rare in adults, are one ofthe most common neoplasms in children and adolescents. Extremities are unusual sites of originfor rhabdomyosarcomas and usually associated with unfavorable outcome. Complete surgicalremoval of the tumor represents a major factor in terms of survival.Our study presents the case of primary alveolar rhabdomyosarcoma of the left hand in a 22 yearsold male who was treated by fifth ray amputation after an incomplete tumor excision. The patient is still tumor-free after 4 years following operation

Keywords

Hand, hypothenar, tumor, sarcoma, rhabdomyosarcoma, amputation

Elde Alveolar Rabdomyosarkom: Yumuşak Doku Sarkomlarinda Oldukça Nadir Bir Olgu

Abstract

Ekstremitelerin yumuşak doku sarkomları çok nadir ve oldukça kötü bir prognoza sahiptir.Rabdomyosarkomlar yumuşak doku sarkomu olup, erişkin yaşta nadir olarak görülürler, dahasıklıkla çocukluk ve ergenlik dönemi tümörleridir. Ekstremite tutulumu rabdomyosarkomlariçin alışılmadık bölgeler olup ve genellikle kötü sonuçlarla ilişkilidir. Sağ kalım açısından majorfaktör tümörün cerrahi olarak tamamen çıkarılmasıdır.Vakamız 22 yaşında erkek bir hastanın sol elinde çıkan primer alveolar rabdomyosarkomununinkomplet tümör eksizyonu sonrasında 5. ray ampütasyon ile tedavisini anlatılmaktadır. Hastanın ameliyat sonrası 4 yıllık takiplerinde tümör dokusu saptanmamıştır

Keywords

El, hipotenar, tumor, sarkom, rabdomyosarkom, amputasyon

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