Bland-White-Garland Sendromlu Olguda Seçilebilir Bir Cerrahi Teknik

Year 2020, Volume: 22 Issue: 2, 131 - 133, 30.08.2020

Ata Niyazi Ecevit Nur Dikmen Yaman , Burcu Arıcı Zeynep Eyıleten Bülent Kaya , Mustafa Adnan Uysalel

https://doi.org/10.18678/dtfd.687919

Abstract

Sol koroner arterin pulmoner arterden orijin alması (ALCAPA) nadir olmakla birlikte, ilk olarak 1866’da tarif edilen bir major konjenital kardiyak anomalidir. Sol koroner arterin direkt aortaya reimplantasyonu ve koroner arter baypas greftleme prosedürleri de dahil olmak üzere çok sayıda cerrahi teknik ikili koroner arteriyel sistem oluşturmayı amaçlamaktadır. Sol koroner arter nadir olarak non-facing pulmoner sinüsten köken alır ve bu nativ aortaya uzak mesafede bir bölge olduğu için, direkt reimplantasyonun teknik olarak oldukça zor olduğu cerrahi onarımdır. Bu vaka sunumunda, non-facing pulmoner sinus kökenli sol koroner arterin, otolog pulmoner arter duvarından tünel oluşturularak aortaya rekonstrüksiyonu cerrahi tekniği bir seçenek olarak sunulmuştur.

Keywords

ALCAPA, koroner arter anomalisi, konjenital kalp hastalığı

An Eligible Surgical Repair Technique for Bland-White-Garland Syndrome

Abstract

Anomalous origin of left coronary artery from pulmonary artery (ALCAPA) is an uncommon but major congenital cardiac anomaly, which was firstly defined in 1866. Multiple surgical techniques intend to compose 2-coronary artery system, including direct reimplantation of left coronary artery to aorta and coronary artery bypass grafting procedures. Left coronary artery seldomly rises from non-facing pulmonary sinus, where direct reimplantation is technically quite difficult for surgical correction because of long distance from native aorta. In this case report, a surgical technique option of reconstructing left coronary artery, arising from non-facing sinus which we turned to aorta with a tunnel created from autologous pulmonary artery wall, was presented.

Keywords

ALCAPA, coronary artery anomaly, congenital heart disease

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