Fahr’s Syndrome presented with vertigo

Abstract

Fahr\'s syndrome is a entity characterized by clinical and neuro-imaging findings. A 36-year-old man presented to emergency room with vertigo that started 3 days ago. On his neurologic examination there were horizontal nystagmus, dysmetria and ataxia. Blood calcium was lower than normal levels (5.3 mg/dl). He had seizures since the age of 17. We thought that patient diagnose Fahr\'s syndrome and got brain CT. Calcifications on brain CT were most prominent in dentate nucleus and bilateral basal ganglia. These patients diagnosed usually accidentally but we present a case presented with vertigo complaint and then diagnosed Fahr\'s syndrome.

Keywords

• Fahr’s syndrome, vertigo, emergency room

Fahr’s Syndrome presented with vertigo

Öz

Fahr sendromu klinik ve nöro-görüntüleme bulguları ile karakterize bir tablodur. 36 yaşında, erkek hasta 3 gün önce başlayan vertigo ile acil servise başvurdu. Nörolojik muayenesinde horizontal nistagmus ve ataksi vardı. Serum kalsiyum seviyesi normalden daha düşüktü (5.3 mg/dl). 17 yaşından bu yana nöbet geçiriyordu. Hastanın Fahr sendromu olabileceğini düşünerek beyin BT çektirdik. Beyin BT’de dentate nükleuslarda ve bilateral bazal ganglionlarda belirgindi. Bu hastalar sıklıkla tesadüfen tanı almakta olmasına rağmen vakamız vertigo ile başvurmuş ve Fahr sendromu tanısı almıştır

Anahtar Kelimeler

• Fahr sendromu, vertigo, acil servis

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