Prımary Renal Malignant Fibrous Histiocytoma

Abstract

Malignant fibrous histiocytoma (MFH) is the most common soft tissue sarcoma in adults occurring in the extremities and retroperitoneum. However, primary MHF of the kidney is extremely rare. Clinical, and histopathological diagnosis of MFH creates difficulties both for urologists, and pathologists. Herein, we aim to present this rarely seen lesion, and discuss its clinical, and radiological prognosis, as well as its histopathological and clinical diagnosis.

Keywords

• Malignant fibrous histiocytoma, kidney, treatment

Prımary Renal Malignant Fibrous Histiocytoma

Öz

Malign fibröz histiyostom, adultlarda retroperitonum ve ekstremitelerde oluşan en yaygın yumuşak doku sarkomudur. Ancak böbreğin primer malign fibröz histiyositomu oldukça nadirdir. Malign fibröz histiyositomun klinik ve histopatolojik tanısı ürologlar ve patologların her ikisi içinde zorluklar oluşturur. Burada histopatolojik ve klinik tanısının yanısıra, klinik ve radyolojik prognozunu tartışarak bu nadir görülen leyzonu sunmayı amaçladık

Anahtar Kelimeler

• Malign fibröz histiyositom, böbrek, tedavi

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