Ciddi Aneminin Beklenmeyen Bir Nedeni: Endometrial Stromal Sarkoma; Olgu Sunumu

Year 2022, , 31 - 34, 29.03.2022

Alperen Aksan Burcu Gündoğdu Öztürk , Berna Dilbaz

https://doi.org/10.46969/ezh.928000

Abstract

Endometrial stromal sarkom (ESS), genellikle perimenopozal kadınlarda görülen uterusun nadir bir malign tümörüdür. Bu olguda akut ağır vajinal kanama ve şiddetli anemi ile başvuran 42 yaşında jinekolojik muayeneyi ve endometriyal örneklemeyi reddeden bir kadın hastayı ele aldık. Transabdominal ultrasonografik değerlendirmede uterusun fundal bölgesinde 9x6 cm boyutlarında intramural submuköz kitle tespit edildi. ESS tanısı, ameliyat öncesi leiomyom olduğu düşünülen tümörün frozen kesiti ile tesadüfen konuldu. Jinekolojik Onkoloji Bölümü ile intraoperatif konsültasyon sonrası total histerektomi ve bilateral salpenjektomi yapıldı. Nihai patolojik raporun ardından hastaya tedavinin sonlandırılması için bilateral ooferektomi önerildi.

Keywords

Endometrial stromal sarkom (ESS), malign tümör, endometrium

Supporting Institution

Destekleyen kurum bulunmamaktadır.

An Unexpected Cause of Severe Anemia: Endometrial Stromal Sarcoma; Case Report

Abstract

Endometrial stromal sarcoma (ESS) is a rare malignant tumour of the uterus that usually occurs in perimenopausal women. Such a case was a hospitalized 42-year-old woman with acute heavy vaginal bleeding and severe anaemia. The patient refused to have a gynaecological examination and endometrial sampling. However, during the transabdominal ultrasonographic evaluation, an intramural submucous mass of 9 cm × 6 cm was detected in the fundal area of the uterus. The diagnosis of ESS was discovered unexpectedly by examining a frozen section of the tumour that was thought to be leiomyoma preoperatively. After intraoperative consultation with the Gynaecologic Oncology Department, total hysterectomy and bilateral salpingectomy were performed. Once the final pathological report was presented, the patient was recommended to have bilateral oophorectomy in order to proceed with the treatment.

Keywords

Endometrial stromal sarcoma (ESS), malignant tumour, endometrium

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