Low-grade fibromyxoid sarcoma: a rare condition with high proliferation

Year 2018, , 238 - 241, 04.07.2018

Marzieh Karimi Khezri M. Özgür Taşkapılıoğlu Alper Türkkan Ulviye Yalçınkaya Ahmet Bekar

https://doi.org/10.18621/eurj.339764

Abstract

Low-grade fibromyxoid sarcoma
(LGFMS) is a type of high metastatic potential of the fibrosarcomas. Most
of the time there is a long interval between tumor presentation and metastasis.
We present 2 cases of LGFMS. The first is a 31-year-old female with a mass in
anterior aspect of her left thigh, and the other is a 68-year-old female with
mass in posterior of her neck. Both cases underwent operation for several times
and confirmed as LGFMS histopathologically, there is no exact protocol for
postoperative follow-up to detect early metastases according to the relative variety
of LGFMS. So informing the patients about the long-standing metastatic
potential of their disease is important. 

Keywords

fibrosarcoma, low-grade fibromyxoid sarcoma, surgery

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