Congenital adrenal hyperplasia with an ovarian adrenal rest tumor: a case report

Year 2020, Volume: 6 Issue: 1, 77 - 82, 04.01.2020

Betül Aydın Buyruk , Göknur Yorulmaz , Ayşe Nur Değer Medine Nur Kebapçı

https://doi.org/10.18621/eurj.435638

Abstract

Adrenal
rest tumors (ART) are extra-adrenal findings of adrenal tissue. Testicular
adrenal rest tumors (TART) are widespread in males with congenital adrenal
hyperplasia (CAH). Ovarian adrenal rest tumours (OART), which form in females
with CAH, are less commonly seen. Reports in literature of OART are extemely
rare. The case is here presented of a 43-year-old female who was diagnosed at
the age of 15 years with CAH and underwent bilateral adrenalectomy at the age
of 37. On presentation at our clinic, 4×2 cm mass was determined on the right
adnexa in the advanced tests and a right-side salpingo-oopherectomy was
performed. The pathology examination reported heterotopic adrenal cortical
tissue. Routine ovarian imaging in females with CAH is not indicated. Although
OART are rarely seen, they should be kept in mind and these patients should be
evaluated radiologically together with laboratory tests. 

Keywords

Ovarian adrenal rest tumor, congenital adrenal hyperplasia

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