Year 2020, Volume 6 , Issue 1, Pages 77 - 82 2020-01-04

Congenital adrenal hyperplasia with an ovarian adrenal rest tumor: a case report

Betül AYDIN BUYRUK [1] , Göknur YORULMAZ [2] , Ayşe Nur DEĞER [3] , Medine Nur KEBAPÇI [4]


Adrenal rest tumors (ART) are extra-adrenal findings of adrenal tissue. Testicular adrenal rest tumors (TART) are widespread in males with congenital adrenal hyperplasia (CAH). Ovarian adrenal rest tumours (OART), which form in females with CAH, are less commonly seen. Reports in literature of OART are extemely rare. The case is here presented of a 43-year-old female who was diagnosed at the age of 15 years with CAH and underwent bilateral adrenalectomy at the age of 37. On presentation at our clinic, 4×2 cm mass was determined on the right adnexa in the advanced tests and a right-side salpingo-oopherectomy was performed. The pathology examination reported heterotopic adrenal cortical tissue. Routine ovarian imaging in females with CAH is not indicated. Although OART are rarely seen, they should be kept in mind and these patients should be evaluated radiologically together with laboratory tests. 

Ovarian adrenal rest tumor, congenital adrenal hyperplasia
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Primary Language en
Subjects Endocrinology and Metabolism
Journal Section Case Reports
Authors

Orcid: 0000-0003-3476-3877
Author: Betül AYDIN BUYRUK (Primary Author)
Institution: Department of Endocrinology, Osmangazi University School of Medicine, Eskişehir, Turkey
Country: Turkey


Orcid: 0000-0001-8596-9344
Author: Göknur YORULMAZ
Institution: Department of Endocrinology, Osmangazi University School of Medicine, Eskişehir, Turkey
Country: Turkey


Orcid: 0000-0001-9674-0799
Author: Ayşe Nur DEĞER
Institution: Department of Endocrinology, Dumlupınar University, Kütahya Evliya Çelebi Training and Research Hospital, Kütahya, Turkey
Country: Turkey


Orcid: 0000-0002-8286-5256
Author: Medine Nur KEBAPÇI
Institution: Department of Endocrinology, Osmangazi University School of Medicine, Eskişehir, Turkey
Country: Turkey


Dates

Publication Date : January 4, 2020

EndNote %0 The European Research Journal Congenital adrenal hyperplasia with an ovarian adrenal rest tumor: a case report %A Betül AYDIN BUYRUK , Göknur YORULMAZ , Ayşe Nur DEĞER , Medine Nur KEBAPÇI %T Congenital adrenal hyperplasia with an ovarian adrenal rest tumor: a case report %D 2020 %J The European Research Journal %P -2149-3189 %V 6 %N 1 %R doi: 10.18621/eurj.435638 %U 10.18621/eurj.435638