The Case of Nonimmune Hydrops Fetalis Due to Simple Lung Cyts

Abstract

Nonimmune hydrops fetalis (NIHF) is a serious fetal condition in which abnormal fluid accumulates in at least two different fetal compartments, and in which circulating antibodies against fetal red-cell antigens are absent in the mother. NIHF is mostly associated with chromosomal disorders, cardiac malformations, arrhythmias, fetal anaemia and TORCH infections. The incidence of NIHF is approximately 1:2500 to 1:3500 births, although in some series the incidence is as high as approximately 1 in 200 pregnancies. Still, the prognosis in NIHF is poor, with perinatal mortality rates that range from 50% to more than 90% in several series. In this case, we desired to emphasize the importance of revising prognostic factors and to draw attention to early intrauterin intervention in NIHF due to simple lung cyst.

Keywords

• Simple lung cyst, Nonimmune hydrops fetalis, Prognosis, Intrauterin intervention.

Basit Akciğer Kistine Bağlı Non-İmmün Hidrops Fetalis Olgusu

Öz

Non-immun hidrops fetalis (NİHF), annede fetal eritrositlere karşı dolaşan antikorların olmadığı ve en az iki fetal kompartmanda anormal sıvı toplanmasının olduğu ciddi fetal durumdur. NİHF etiyolojisinde kromozom anomalileri, kardiak yapısal malformasyonlar, aritmiler, fetal anemi ve TORCH infeksiyonlarının sık görüldüğü mortalitesi yüksek bir tablodur. NİHF insidansı her ne kadar bazı serilerde hamilelikte yaklaşık 1/200 kadar yüksek olsa da doğumdaki insidansı yaklaşık olarak 1:2500-1:3500'dir. NİHF'de prognoz, çeşitli serilerde %50-90'a kadar olan perinatal mortalite oranlarıyla halen kötüdür. Biz bu olguda, basit akciğer kistine bağlı NİHF'de erken intrauterin müdehaleye dikkat çekmek ve prognostik faktörlerin tekrar gözden geçirilmesinin gerekliliğini vurgulamak istedik.

Anahtar Kelimeler

• Basit akciğer kisti, Non-immün hidrops fetalis, Prognoz, Intrauterin müdahale.

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