Hirayama Hastalığı (Monomelik Amyotrofi)

Year 2008, Volume: 13 Issue: 4, 274 - 276, 01.08.2008

Tahir Kurtuluş Yoldaş Yıldız Çoruh Hava Dönmez Keklikoğlua Hayriye Gül Polat Bülent Güven

https://izlik.org/JA57HB42NE

Abstract

Hirayama Hastalığı (HH), genç erkeklerde daha sık görülen benign bir alt motor nöron hastalığıdır. Distal ekstremiteyi tutan ilerleyici güçsüzlük ve sinsi başlangıç ile karekterizedir. Genellikle başlangıcından sonra 5 yıl içinde stabilize olan, benign ve nonprogresif bir hastalık olarak kabul edilir. Biz bu bildiride duysal yakınmanın eşlik etmediği progresif amyotrofi bulguları olan 23 yaşında bir kadın hastayı sunuyoruz.©2008, Fırat Üniversitesi, Tıp Fakültesi

Keywords

Hirayama hastalığı , monomelik amyotrofi , motor nöron hastalığı

Hirayama Disease (Monomelic Amyotrophy)

https://izlik.org/JA57HB42NE

Abstract

Hirayama Disease (HD) is a benign lower motor neuron disorder in the young with male preponderance. It is characterized by insidious onset and progressive weakness and wasting of a distal extremity . Generally, this disease is considered a 'benign' and non-progressive motor neuron disease, which stabilizes within five years of onset.We describe a 23-year-old famele patient who experienced progressive amyotrophy with no sensorial abnormality.©2008, Firat University, Medical Faculty.

Keywords

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• Kabul Tarihi:22.11.2007