Anaesthesia For Friedreich Ataxia

Abstract

Friedreich Ataxia is a rare, hereditary, neurodegenerative disease. Neurologic findings are dominant although there are pulmonary, cardiac and endocrine findings. Because its motor neuron disorder, neuromuscular blockers must be used carefully. We want to explain the approach of the anaesthesia for the 24 years old female patient with Friedreich Ataxia is operated on account of the acute appendicitis.©2008, Firat University, Medical Faculty.

Keywords

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Friedreich Ataksisinde Anestezi

Öz

Friedreich ataksisi nadir görülen, herediter, nörodejeneratif bir hastalıktır. Kardiyak, pulmoner ve endokrin bulgular görülmekle beraber nörolojik bulgular ön plandadır. Motor nöron hastalığı olmasından dolayı kas gevşetici kullanımına özel dikkat gerektirmektedir. Sunumuzda akut apandisit nedeniyle opere edilen Friedreich ataksili 24 yaşındaki kadın hastada anestezik yaklaşımımızı aktarmak istedik.©2008, Fırat Üniversitesi, Tıp Fakültesi

Anahtar Kelimeler

• Friedreich ataksisi, anestezi, nöromüsküler blokörler

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13. Kabul Tarihi:17.09.2007