Solitary Tracheal Neurofibroma: Case Report and Literature Review

Abstract

Tracheal neurofibroma (TN) is a slow-growing benign tumor, which can be confused with malignant tumors of the trachea clinically, radiologically and macroscopically. Tracheal location of solitary neurofibromas is extremely rare, with only 18 cases reported hitherto. A 65-year-old male case was admitted to the emergency department in January 2005, complaining of shortness of breath both at rest and on effort, expectorating sputum and cough continuing for 15 days. The patient, whose mass was totally excised, was diagnosed as “solitary tracheal neurofibroma”. TN, which is usually accompanied with NF1, has very rare solitary forms. We aimed to discuss this case in the light of literature data, due to its being rare and posing a distinctive diagnosis problem.©2008, Firat University, Medical Faculty.

Keywords

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Soliter Trakeal Nörofibrom: Olgu Sunumu ve Literatürün Gözden Geçirilmesi

Öz

Trakeal nörofibrom (TN), yavaş büyüyen, klinik, radyolojik ve makroskobik olarak trakeanın malign tümörleri ile karışabilen benign bir tümördür. Soliter nörofibromların trakeal yerleşimi oldukça nadir olup bu güne kadar bildirilen olgu sayısı 18' dir. Olgu 65 yaşında erkek hasta, 15 gündür devam eden, efor ve istirahatle gelen nefes darlığı, balgam çıkarma, öksürük yakınmaları ile acil servise başvurdu. Hastada endotrakeal kitle saptandı. Kitlesi total eksize edilen hastaya “soliter trakeal nörofibrom” tanısı kondu. TN genellikle NF1 ile birlikte olup soliter formları oldukça nadir görülmektedir. Olgunun nadir görülmesi ve ayırıcı tanı problemi oluşturması nedeni ile literatür eşliğinde tartışmayı amaçladık.©2008, Fırat Üniversitesi, Tıp Fakültesi.

Anahtar Kelimeler

• Trakea, Soliter Nörofibrom

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