Year 2021, Volume 8 , Issue 1, Pages 39 - 51 2021-04-30

Etiological Factors and Audiological Evaluation of Children with Congenital Unilateral Hearing Loss

İlkem KARA [1] , Mine BAYDAN [2] , Bilgehan BÖKE [3] , Gamze ATAY [4] , Burçe ÖZGEN MOCAN [5] , Gülsüm GENÇ [6]

Objectives: The aim of the present study is to evaluate the audiological, radiological, and etiological in terms of clinical findings relating to babies and children with congenital unilateral hearing loss. Materials and Methods: Audiometric tests, tympanometric and acoustic reflex measurements, otoacoustic emission tests, and auditory brainstem response assessments were conducted. Twenty-nine babies and children (13 F ;16 M) diagnosed with congenital unilateral hearing loss, between the ages of 3–87 months, were included in this study. Results: Of these patients, 65.5% (n:19) were diagnosed with sensorineural hearing loss and 34.5% (n:10) with conductive hearing loss. Of the subjects with sensorineural hearing loss, 57.9% were diagnosed with profound hearing loss. Of the subjects with conductive hearing loss, 7 of the 10 (70%) had been diagnosed with microtia. Of the patients with conductive hearing loss, all those who had received CT scans were diagnosed with ossicular chain malformations. The most frequent risk factor for sensorineural hearing loss is intermarriage (26.3%), whereas the most frequent risk factor for conductive hearing loss is craniofacial anomalies (30%). Conclusion: The interdisciplinary work in otology, audiology, and radiology is essential for early diagnosis and effective treatment of congenital unilateral hearing loss cases.
unilateral hearing loss, congenital, audiologic findings
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Primary Language en
Subjects Health Care Sciences and Services
Journal Section Articles

Orcid: 0000-0001-9786-4769
Author: İlkem KARA
Country: Turkey

Orcid: 0000-0003-2836-0799
Author: Mine BAYDAN (Primary Author)
Country: Turkey

Orcid: 0000-0002-5249-938X
Author: Bilgehan BÖKE
Country: Turkey

Orcid: 0000-0002-7740-1641
Author: Gamze ATAY
Country: Turkey

Orcid: 0000-0003-0758-2712
Author: Burçe ÖZGEN MOCAN
Country: Turkey

Orcid: 0000-0002-7200-4384
Author: Gülsüm GENÇ
Country: Turkey


Application Date : June 9, 2020
Acceptance Date : February 22, 2021
Publication Date : April 30, 2021

APA Kara, İ , Baydan, M , Böke, B , Atay, G , Özgen Mocan, B , Genç, G . (2021). Etiological Factors and Audiological Evaluation of Children with Congenital Unilateral Hearing Loss . Hacettepe University Faculty of Health Sciences Journal , 8 (1) , 39-51 . Retrieved from