WILLIAMS BEUREN SYNDROME, A SHORT COMMUNICATION OF A PECULIAR CASE

Year 2023, , 108 - 111, 25.08.2023

Michele Callea

https://doi.org/10.61139/ijdor.1282837

Abstract

Williams-Beuren syndrome (WBS) is a rare congenital disorder that includes cardiovascular problems, mental retardation, distinctive facial features and dental anomalies. This case report the treatment of a tooth fracture after dental trauma in a 13-year-old male with WBS syndrome. Intraoral clinical examination revealed anterior interdental space and enamel hypoplasia in incisors. Dental treatment included: The fracture tooth fragment was restored after basic behavioral orientation

Keywords

Williams-Beuren syndrome, tooth fracture, tooth anomalies

References

• 1. Ferreira SB, Viana MM, Maia NG, Leão LL, Machado RA, Coletta RD, de Aguiar MJ, Martelli-Júnior H.Oral findings in Williams-Beuren syndrome. Med Oral Patol Oral Cir Bucal. 2018;23(1):e1-e6
• 2. Matsuno S, Tsuji M, Hikita R, Matsumoto T, Baba Y, Moriyama K. Clinical study of dentocraniofacial characteristics in patients with Williams syndrome. Congenit Anom (Kyoto). 2019;59(5):162-168.
• 3. Cogulu D, Hazan F, Dindaroglu FC. Orofacial Findings and Dental Management of Williams Syndrome. Genet Couns. 2015;26(4):437-42.
• 4. Hertzberg J, Nakisbendi L, Needleman HL, Pober B.Williams syndrome--oral presentation of 45 cases. Pediatr Dent. 1994;16(4):262-7.
• 5. Castro T, de Paula Martins Santos C, de Oliveira Lira Ortega A, Gallottini M.Oral characteristics and medical considerations in the dental treatment of individuals with Williams syndrome. Spec Care Dentist. 2019;39(2):108-113.
• 6 Axelsson S, Bjørnland T, Kjaer I, Heiberg A, Storhaug K. Dental characteristics in Williams syndrome: a clinical and radiographic evaluation. Acta Odontol Scand. 2003;61(3):129-36.
• 7. Axelsson S. Variability of the cranial and dental phenotype in Williams syndrome. Swed Dent J Suppl. 2005;(170):3-67.
• 8. Çitir M, Zengin AZ. Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. Turkiye Klinikleri. Dishekimligi Bilimleri Dergisi, 2019;25(3): 371-374.
• 9. Hertzberg J, Nakisbendi L, Needleman HL, Pober B. Williams syndrome–oral presentation of 45 cases. Pediatr Dent. 1994;16(4):262–267
• 10. Morris CA, Braddock SR, AAP COUNCIL ON GENETICS. Health Care Supervision for Children With Williams Syndrome. Pediatrics. 2020;145(2):e20193761
• 11. Andrade NS, Santos C, Castro T, Gallottini M. Medical considerations in dental treatment of patients with Williams-Beuren syndrome: report of four clinical cases. Clin Lab Res Dentistry. 2015; 21: 7.
• 12. Stefan Axelsson, Tore Bjørnland, Inger Kjær, Arvid Heiberg, Kari Storhaug (2003) Dental characteristics in Williams syndrome: a clinical and radiographic evaluation, Acta Odontologica Scandinavica, 2003;61(3): 129-136.
• 13.Torres CP, Valadares G, Martins MI, Borsatto MC, Díaz-Serrano KV, de Queiroz AM. Oral findings and dental treatment in a child with Williams-Beuren syndrome. Braz Dent J. 2015;26(3):312-6.