Ganglioglioma: A case report

Abstract

Gangliogliomas are mixed neuronal-glial type tumors of the central nervous system (CNS). Gangliogliomas are rare tumors that present histological features and biological behavior of low-grade malignancy. Gangliogliomas account for about 0.5% of all CNS tumors, and they generally occur in childhood. Gangliogliomas make up about 8.0% of CNS tumors in children. These tumors are mostly localized in the supratentorial region and often present with seizures. Surgery is the first choice of treatment. We present a case of a 14-yearold male who presented with headache, with vomiting added recently. A left temporal mass was detected during investigations. The mass was totally resected surgically. The pathology was reported as ganglioglioma. The patient is being followed sufficiently in our clinic.

Keywords

• Ganglioglioma,Adolescent,Male,Radiotherapy,Magnetic Resonance Imaging,Surgical Procedures, Operative

Gangliogliom: Olgu sunumu

Öz

Gangliogliomlar, merkezi sinir sisteminin (MSS) mikst nöronal glial tümörlerindendir. Nadir görülen bu tümörler, histolojik özellik ve biyolojik davranış olarak düşük derece malignite gösterirler. Gangliogliomlar, tüm MSS tümörlerinin yaklaşık %0,5'ini oluştururlar. Genellikle çocukluk çağında görülürler. Çocuklardaki MSS tümörlerinin yaklaşık %8'ini oluştururlar. Daha sıklıkla supratentorial yerleşim gösteren bu tümörler, en sık nöbet şikayetine yol açarlar. Cerrahi, tedavide ilk seçenektir. Bu yazıda, baş ağrısı ve kusma yakınmaları olan 14 yaşındaki erkek hasta sunuldu. Yapılan incelemeler sonucunda olguda sol temporal kitle saptandı. Kitle, ameliyatla total rezeke edildi. Patoloji incelemesinde gangliogliom olarak rapor edildi. Olgunun takibine devam edilmektedir.

Anahtar Kelimeler

• Cerrahi, gangliogliom, radyoterapi

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