Anesthetic management in VACTERL syndrome

Abstract

VACTERL Syndrome consists of many problems regarding to anesthesia management due to multiple congenital malformations which may include vertebral, cardiac, trachea-osephageal, renal and limb anomalies. Here we present our anesthetic management -in terms of preanesthetic evaluation, premedication, induction and maintenance of anesthesia and postoperative follow up- in a newborn patient with VACTERL Syndrome undergoing tracheo-eosophagial fistula operations. J Clin Exp Invest 2014; 5 (1): 103-105

Keywords

• VACTERL syndrome, anesthesia, ketamin..

VACTERL sendromunda anestetik yaklaşım

Öz

Çoklu konjenital malformasyonlardan dolayı VACTERL sendromunda anestezi yönetimi vertebra, kardiyak, trakea-özefageal, renal ve ekstremite anomalileri nedeniyle bir çok problemi içermektedir. Bu yazıda trakeo-özefageal fistül nedeniyle opere olan VACTERL sendromlu hastamızdaki anestezi öncesi değerlendirme, premedikasyon, anestezi indüksiyonu ve devamı ile postoperatif izlemi içeren anestezi yönetimimizi sunmayı amaçladık.

Anahtar Kelimeler

• VACTERL sendromu, anestezi, ketamin

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