Anesthesia for scoliosis surgery in a patient with arthrogryposis multiplex congenita

Abstract

Arthrogryposis multiplex congenita is a disease which is characterized by congenital multiple joint contractures. This disease with its risks of difficult airway, difficult intra­venous access and malign hypethermia attack is a chal­lenging condition for anesthesiologists. In this paper, we report our anesthetic management experience for scolio­sis surgery in a case with arthrogryposis multiplex con­genita. J Clin Exp Invest 2013; 4 (1): 113-115

Keywords

• Anesthesia, general; Arthrogryposis; Scolio­sis

Artrogripozis multipleks konjenitalı bir hastada skolyoz cerrahisi için anestezi

Öz

Artrogripozis multipleks konjenita, konjenital multipl ek­lem kontraktürleri ile karakterize bir hastalıktır. Bu hastalık zor havayolu, zor intravenöz damaryolu ve malign hiper­termi riski taşıdığı için anestezistler için dikkat edilmesi gereken bir durumdur. Biz bu makalede, skolyoz cerrahisi için anestezi uyguladığımız artrogripozis multipleks kon­jenitalı bir olgudaki anestezi deneyimimizi sunuyoruz.

Anahtar Kelimeler

• Anestezi, genel, artrogripozis, skol­yoz

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