A Neglected case admitted with paraplegia: An intradural extramedullary epidermoid cyst

Öz

Spinal epidermoid tümörler, spinal tümörlerin %1.5-2'sini oluşturan nadir tümörlerdir. Servikal ve torasik spinal kord epidermoid tümörleri oldukça nadirdir. Bu yazıda polikliniğimize üriner inkontinans ve paraparezi ile başvuran torasik bölgede intradural ekstramedüller epidermoid kist tespit edilen 28 yaşında bir olgu sunuldu. Hastanın ilk şikayetleri 16 yıl önce başlamış. Bu dönemde hastaya peroneal muskuler atrofi teşhisi konulmuş ve ayrıntılı tetkik edilememiş. Geç tanı ve tedavi nedeniyle başarılı cerrahi ve kapsamlı fizik tedaviye rağmen mevcut paraparezi ve üriner inkontinans düzelmedi. Spinal epidermoid tümörlerin prognozu histolojik olarak benign oldukları için iyidir. Erken teşhis edilirse tam cerrahi rezeksiyon hastaya iyi nörolojik sonuç sağlar. Nörolojik defisiti mevcut olan hastaların kapsamlı araştırılması ve en erken sürede teşhis konulması hayati önem taşımaktadır.

Anahtar Kelimeler

• Epidermal kist, omirilik sıkışması, omirilik neoplazileri, parapleji, erken tanı

A Neglected case admitted with paraplegia: An intradural extramedullary epidermoid cyst

Abstract

Spinal epidermoid tumors are rare tumors, constituting about 1.5-2% of the spinal tumors. Cervical and thoracic spinal cord epidermoid tumors are exceedingly rare. We reported a case of a 28-year-old patient with an intradural extramedullary epidermoid cyst at the thoracic region presented with urinary incontinence and paraparesis to our outpatient clinic. First symptoms of patient started 16 years ago and diagnosed as peroneal muscular atrophy and he couldn\'t be investigated sufficiently. Because of the delayed diagnosis and treatment, paraparesis and urinary incontinence were persistent in spite of successful surgery and proper physical therapy. Spinal epidermoid tumors have a good prognosis, as they are histologically benign. When diagnosed early, complete surgical resection offers the patient good neurologic outcome. It is important to investigate extensively patients with neurological deficits and to make diagnosis as soon as possible. J Clin Exp Invest 2012; 3(2): 270-272

Keywords

• Epidermal cyst, spinal cord compression, spinal cord neoplasms, paraplegia, early diagnosis

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