Anesthesia management in a pediatric patient with Dandy-Walker syndrome

Abstract

General anesthesia management of patients with Dandy-Walker syndrome is important since intubation may be difficult due to concomitant anomalies such as hydrocephalus, micrognathia and cleft palate. It should be considered that these patients may require postoperative intensive care support. In this article, anesthesia management of a patient with Dandy-Walker syndrome underwent persistent ventriculo-peritoneal shunt was presented.

Keywords

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Dandy-Walker sendromlu çocuk hastada anestezi yönetimi

Öz

Dandy-Walker sendromlu hastalarda genel anestezi yönetimi, hidrosefali, mikrognati ve yarık damak gibi eşlik eden anomaliler nedeniyle zor entübasyon olabileceğinden dolayı önemlidir. Bu hastalarda postoperatif yoğun bakım desteği gerekebileceği akılda tutulmalıdır. Bu makalede kalıcı ventrikülo-peritoneal şant nedeniyle opere edilen Dandy-Walker sendromlu hastanın anestezi yönetimi sunulmuştur.

Anahtar Kelimeler

• Dandy-Walker sendromu, ventriküloperitoneal şant, zor entübasyon

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