A case with catecholaminergic polymorphic ventricular tachycardia

Abstract

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a rare type of polymorphic ventricular tachycardias in individuals without structural cardiac abnormalities. It typically has been induced by exercise or emotional stres. It generally is seen in childhood and adolescent period but rarely is seen in elderly. It usually ends by spontaneus, but rarely cause hemodynamic collapse. In here, we present a case with CPVT of successful treatment with a beta blocker therapy.

Keywords

• Catecholaminergic, ventricular tachycardia

Katekolaminerjik polimorfik ventrikül taşikardili bir olgu

Öz

Katekolaminerjik polimorfik ventrikül taşikardisi yapısal kalp hastalığı yokluğunda görülen polimorfik ventrikül taşikardilerinin nadir bir çeşididir. Tipik olarak egzersiz ya da emosyonel stres tarafından indüklenir. Sıklıkla çocukluk ve adölesan dönemde görülmekle birlikte ilerleyen yaşlarda da açığa çıkabilir. Genellikle kendiliğinden sonlanır, fakat nadiren hemodinamik kollapsa neden olabilir. Burada katekolaminerjik ventrikül taşikardisi tanısı konulup beta bloker tedavi ile başarılı tedavisi yapılan bir olgu sunuldu.

Anahtar Kelimeler

• Katekolaminerjik, ventrikül taşikardisi

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