Hypertension and multiple arterial changes in a child with Klippel Trenaunay syndrome

Year 2014, Volume: 5 Issue: 4, 610 - 613, 01.12.2014

Meral Torun Bayram Önder Yavaşcan Aytaç Gülcü Nejat Aksu Salih Kavukçu Alper Soylu

https://doi.org/10.5799/ahinjs.01.2014.04.0469

Cited By: 1

Abstract

Klippel-Trenaunay syndrome (KTS) is an inherited disorder which essentially affects the venous system. Arterial malformations accompanying venous pathologies are extremely rare. We report a 10-year-old boy of KTS patient presented with hypertension and renal atrophy who have also multiple arterial (renal, pulmonary and internal carotid) pathologic features. J Clin Exp Invest 2014; 5 (4): 610-613

Keywords

Hypertension, arterial changes, Klippel-Trenaunay syndrome

Klippel-Trenaunay sendromlu bir çocukta hipertansiyon ve multipl arteriyel değişiklikler

Abstract

Klippel-Trenaunay sendromu (KTS) özellikle venöz sistemi etkileyen kalıtsal bir hastalıktır. Venöz patolojilere eşlik eden arteriyel malformasyonlar oldukça nadirdir. Biz burada hipertansiyon ve renal atrofi nedeni ile başvuran, multipl arteriyel (renal, pulmoner ve internal karotid) patolojik özelliklere sahip KTS'lu 10 yaşında bir erkek hastayı sunduk.

Keywords

Hipertansiyon, arteriyel değişiklikler, Klippel-Trenaunay sendromu

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