Pierre Robin Sekansı: Yenidoğan Döneminde Hava Yolu Açıklığının ve Beslenmenin Sağlanması

Abstract

Pierre Robin Sekansı PRS , mandibula hipoplazisi, glos- sopitozis ve damak yarığı ile karakterize doğumsal bir anomalidir. Çenenin küçük olması dilin hipofarenkse doğru geriye kaçmasına yol açarak, hava yolu tıkanıklığına neden olabilmekte ve yenidoğan döneminde acil tedavi gerektiren önemli sorunlar ortaya çıkabilmektedir. Hava yolu tıkanıklığına yönelik erken ve uygun yaklaşım yapıl- madığında, gereksiz invaziv girişimler uygulanabilmekte ya da hastalar hipokside kalabilmektedir. Bu makalede, kliniğimizde izlenen PRS tanısı almış vakaların özellikleri, klinik izlemleri verilmiş ve güncel literatür bilgileri ışığın- da tedavi yaklaşımları derlenmiş ve tartışılmıştır

Keywords

• Pierre Robin Sekansı,üst hava yolu tıkanıklığı,yenidoğan canlandırması,hava yolu açılması

Pierre Robin Sequence; Airway Management and Feeding in Newborn

Abstract

Pierre Robin Sequence PRS is a congenital abnormality characterized by the presence of the mandibular hypoplasia glossoptosis and often a cleft palate. Infants with PRS varying degrees of upper airway obstruction and life threatening complication especially in newborn period secondary to micrognathy and posterior displacement of the tongue base. Diagnosis of PRS should be made immediately and the least invasive intervention should be considered before more invasive approaches, to minimize morbidity such as hypoxia. In this article, we evaluated our experience of airway management of PRS cases and discuss optimal airway and feeding management in PRS infant in light of the foregoing literature.

Keywords

• Pierre Robin Sequence,high upper airway obstruction,neonatal resuscitation,airway management

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