Goldenhar sendromlu (okulo-aurikulo-vertebral spektrum) bir olguda gözlenen havayolu problemi

Abstract

Çocuklarda, özellikle 2 yaş altındaki hastalarda ve yenidoğanda, anatomik ve fizyolojik farklılıklar nedeniyle endotrakeal entübasyon ve ventilasyonla ilgili güçlükler daha sık görülmektedir. Özellikle yenidoğan döneminde dil ve oksiput büyük, ağız küçük, epiglot hareketli ve boyun kısa olup bu faktörler laringoskopiyi ve entübasyonu güçleştirebilmektedir. Goldenhar sendromu, etiyolojisi henüz aydınlatılamamış, yaygın sistemik konjenital anomaliler ile karakterize, çoğu kez sporadik nedenlerden kaynaklandığı gözlemlenen bir hastalıktır. Bu olgu sunumunda yenidoğan döneminde yaşadığı solunum sıkıntısı nedeniyle entübe edilmek istenen, ancak havayolu açıklığının sağlanmasında zorluk gelişen 8 aylık Goldenhar sendromlu hastamızın havayolu yönetiminde oluşabilecek güçlükleri tartışmayı planladık.

Keywords

• Goldenhar sendromu,infant,solunum sıkıntısı,entübasyon

Airline problem with a case of Goldenhar syndrome (oculo-auriculo-vertebral spectrum)

Abstract

In children, especially under 2 year-old and newborn, problems about endotracheal intubation and ventilation due to anatomic and physiologic differences are frequently observed. Especially in newborn term, big tongue and occiput, small mouth, mobile epiglottis and short neck may occur. These factors may complicate laryngoscopy and intubation. Goldenhar syndrome, etiology is not clear yet, is a disease which is characterized by common systemic congenital anomalies and it is often observed to be caused by sporadic reasons. In this case report, we aimed to discuss the complications during airway management of an 8 month-old Goldenhar syndrome patient who wanted to be intubated due to respiratory distress in infant term but had difficulty in providing airway. 

Keywords

• Goldenhar syndrome,infant,respiratory distress,intubation

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