CLINICAL AND RADIOGRAPHIC FEATURES OF PARRY-ROMBERG SYNDROME

Year 2017, Volume: 51 Issue: 3, 45 - 49, 02.10.2017

Vidya Ajila Mithula Nair Shruthi Hegde , G Subhas Babu Rumela Ghosh

Abstract

Parry-Romberg syndrome or progressive hemifacial atrophy is a craniofacial disorder characterized by slow and progressive atrophy, generally unilateral, of facial tissues including muscles, bones and skin. The coup de sabre is a clear line of demarcation seen between the normal and abnormal structures. The severity of the facial deformity is dependent on the age of onset of the disease. Cosmetic management is the only available treatment and has to be delayed until facial growth is completed. The present case report deals with a 43-year-old woman with progressive hemifacial atrophy which started from the age of 10 months.  Despite almost complete involvement of the right paramedian area and the early age of onset, she had neither eye changes nor any dental malformations.

Keywords

Parry-Romberg syndrome , progressive atrophy; hemifacial; craniofacial disorder; treatment

References

• Ayyildiz O, Ayyildiz S, Durukan AH, Sobaci G. Progressive hemifacial atrophy with contralateral uveitis: A case report. Iran Red Crescent Med J 2015;17(9):e16168.
• Balan P, Gogineni SB, Shetty SR, D'Souza D. Three-dimensional imaging of progressive facial hemiatrophy (parry-romberg syndrome) with unusual conjunctival findings. Imaging Sci Dent 2011;41(4):183-187.
• Kaya M, Sel Yilmaz C, Kurtaran H, Gunduz M. Chronologic presentation of a severe case of progressive hemifacial atrophy (parry-romberg syndrome) with the loss of an eye. Case Rep Otolaryngol 2014;2014:703017.
• Sudarshan R. Progressive hemi facial atrophy- a review. SEAJCRR 2012;1(1):16-21.
• Deshingkar SA, Barpande SR, Bhavthankar JD, Humbe JG. Progressive hemifacial atrophy (parry-romberg syndrome). Contemp Clin Dent 2012;3(Suppl 1):S78-81.
• Khan M, Khan M, Negi R, Gupta N. Parry romberg syndrome with localized scleroderma: A case report. J Clin Exp Dent 2014;6(3):e313-316.
• Grippaudo C, Deli R, Grippaudo FR, Di Cuia T, Paradisi M. Management of craniofacial development in the parry-romberg syndrome: Report of two patients. Cleft Palate Craniofac J 2004;41(1):95-104.
• Pinheiro TP, Silva CC, Silveira CS, Botelho PC, Pinheiro M, Pinheiro Jde J. Progressive hemifacial atrophy--case report. Med Oral Patol Oral Cir Bucal 2006;11(2):E112-114.
• Erfan M, Khan I, Ahmed AS, Hasnain S. A tale of two diseases: Parry romberg syndrome and en coup de sabre: A case report. Int J Pathol 2015;13(2):82-86.
• Kumar AA, Kumar RA, Shantha GP, Aloogopinathan G. Progressive hemi facial atrophy - parry romberg syndrome presenting as severe facial pain in a young man: A case report. Cases J 2009;2:6776.
• Gomez-Diez SG, Lopez LG, Escobar ML, Gutierrez LJ, Oliva NP. Progressive facial hemiatrophy with associated osseous lesions. Med Oral Patol Oral Cir Bucal 2007;12(8):E602-604.