CLINICAL AND CEPHALOMETRIC ANALYSIS OF THREE CASES WITH PYCNODYSOSTOSIS: CASE REPORTS

Year 2015, Volume: 49 Issue: 1, 51 - 55, 25.03.2015

Eser Çapan , Serap Turan Hülya Kılıçoğlu

https://doi.org/10.17096/jiufd.70673

Abstract

The aim of this article is to present intra- and extra-oral and cephalometric findings of three patients with a rare disease: the pycnodysostosis. Two cases had skeletal Class III malocclusion due to maxillary retrognathia and one had bimaxillary retrusion with Class I relationship. Total circular crossbite, increased gonial angle and vertical facial proportions, deep-narrow palates and retruded upper lip were found in all cases. Maxillary expansion, face mask treatment or/and orthognathic surgery are treatment alternatives, considering the growth and development. Bone fragility and the risk of osteomyelitis after extractions should be considered in such cases before orthodontic treatment and orthognatic surgery.

Keywords

Pycnodysostosis; clinical evaluation; cephalometric evaluation

Piknodizostozisli Üç Olgunun Klinik ve Sefalometrik Analizi: Olgu Sunumu

Abstract

Bu çalışma ender rastlanan piknodizostozisli üç
olgunun ağız dışı ve içi bulguları ile sefalometrik
değerlendirmesini sunmaktadır. Piknodizostozisli
üç olgunun ağız dışı ve ağız içi bulguları klinik
olarak değerlendirilmiş, hastalardan alınan lateral
sefalometrik radyografiler üzerinde iskeletsel ve
dişsel ölçümler gerçekleştirilmiştir. Olguların
ikisinde maksiller retrognatiye bağlı iskeletsel
sınıf III yapı, diğerinde ise bimaksiller retrüzyon
ile beraber sınıf I yapı mevcuttur. Tüm hastalarda
total sirküler çapraz kapanış, artmış gonial açı ve
dik yön yüz boyutları, derin damak kubbesi ile üst
dudakta retrüzyon gözlenmiştir. Bu tip olguların
tedavisinde büyüme-gelişme dönemi de göz önünde
bulundurularak maksiller genişletme, yüz maskesi veya
ortognatik cerrahi tedavi alternatifleri arasındadır.
Piknodizostozisli hastalarda kemik kırılganlığı ve
diş çekimlerinden sonra osteomyelit riskinin yüksek
olması nedeniyle yapılacak ortodontik tedavi ve
ortognatik cerrahi müdahalelerde bu durum gözönüne
alınarak hastaya yaklaşımda bulunulmalıdır.

Keywords

Piknodizostozis, klinik değerlendirme, sefalometrik değerlendirme

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