Orbital plasmasitom

Year 2021, Volume: 2 Issue: 3, 91 - 94, 08.09.2021

Mehmet Zengın , Semiha Baykal Havare , Nevra Dursun , Kadir Kotil

https://doi.org/10.47582/jompac.831801

Abstract

Ekstramedüller plazmasitom nadir görülem plazma hücreli bir neoplazidir. Sıklıkla üst solunum yollarını tutar, göz tutulumu ise son derece nadirdir. Bu bildiride orbital kaynaklı bir ekstramedüller plazmasitom olgusu sunduk. 55 yaşında erkek hasta, sol gözde şişlik nedeniyle yapılan tetkiklerinde orbital yerleşimli 5x6 cm boyutlarında kitle tespit ediliyor. Kitlenin histopatolojik incelemesinde amiloid arasında bol miktarda plazma hücreleri izlenmiş olup kappa-lamda ile monoklonalite görülmüştür. Olgu plasma hücreli neoplazi olarak rapor edilmiş olup tetkiklerinde başka bir odak tesbit edilmediğinden soliter plasmasitom olarak kabul edilmiştir. Ekstramedüller plazmasitom orbital yerleşimli kitlelerde akılda tutulmalıdır. Prognozu farklılık gösterdiği için tanısında sistemik bir plazma hücre diskrazisinin varlığı mutlaka sorgulanmalıdır.

Keywords

Ekstramedüller plazmasitom, plazma hücreli neoplaziler, göz

Supporting Institution

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Project Number

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Thanks

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Orbital plasmasitom

Abstract

Extramedullary plasmacytoma is a rare plasma cell neoplasia. It often involves the upper respiratory tract, eye involvement is extremely rare. In this report, we present a case of extramedullary plasmacytoma of orbital origin. A 55-year-old male patient, an orbitally located mass with a size of 5x6 cm was detected in the examinations performed for swelling in the left eye. In the histopathological examination of the mass, abundant plasma cells among amyloid were observed, and monoclonality with kappa-lambda was observed. The case was reported as plasma cell neoplasia and was accepted as a solitary plasmacytoma since no other focus was detected in the tests. Extramedullary plasmacytoma should be kept in mind in orbitally located masses. Since the prognosis is different, the presence of a systemic plasma cell dyscrasia should be questioned in its diagnosis.

Keywords

Extramedullary plasmacytoma, plasma cell neoplasms, eye

Project Number

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