Sitüs inversüs totalis ve çift superior vena kava: Nadir bir olgu

Öz

Situs inversus totalis (SİT) ve çift superior vena kava (SVK) nadir görülen  Konjenital anomalilerdir. Olguların çoğunluğu başka nedenlerle görüntülemede tesadüfen teşhis edilir. Diğer kardiyak anomalilerle birlikte olmadıkça çift SVK genellikle asemptomatiktir. 22 yaşındaki kadın hasta öksürük, baş ağrısı, halsizlik ve nefes darlığı şikayetleri ile kardiyoloji kliniğine başvurdu. 7 yıl önce atriyal septal defekt ve ventriküler septal defekt cerrahi onarım öyküsü olan hasta pulmoner emboli ve pulmoner hipertansiyon tanısı ile hastaneye yatırıldı. Göğüsün kontrastlı çok kesitli bilgisayarlı tomografisi (BT) kliniğimizde çekildi. BT, SİT ile çift SVK’ı gösterdi. Çift SVK’nın sağ SVK’sı sol atriuma drene idi. Kalp anomalilerinin eşlik ettiği anormal venöz bağlantı varyasyonları ekokardiyografi ve BT ile kombine görüntüleme yaklaşımıyla ameliyattan önce tam olarak tanımlanmalıdır.

Anahtar Kelimeler

• Situs İnversus,Superior Vena Kava,Görüntüleme

Situs inversus totalis with double superior vena cava: An unusual case report

Abstract

Situs inversus totalis (SIT) with double superior vena cava (SVC) is a rare congenital anomaly. Most cases are diagnosed incidentally after imaging for other reasons. Double SVC is usually asymptomatic, unless associated with other cardiac anomalies. A 22-year-old female patient with the complaints of cough, headache, weakness, and shortness of breath was admitted to the cardiology department. The patient, who was hospitalized with a diagnosis of pulmonary embolism and pulmonary hypertension, had a history of surgical repair of atrial septal defect and ventricular septal defect 7 years ago. Contrast-enhanced multislice computed tomography (CT) of the chest was obtained in our department. CT demonstrated SIT with double SVC, with the right SVC draining into the left atrium. The variations of anomalous venous connections accompanying cardiac anomalies should be fully defined before surgery with a combined imaging approach with echocardiography and CT.

Keywords

• Situs Inversus,Superior Vena Cava,Imaging

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