Erişkin bağırsak malrotasyonunda iç organ varyasyonları: Olgu serisi çalışması

Öz

Amaç: İntestinal malrotasyon (IM), midgutta çok nadir görülen rotasyonel bir anomalidir. Nadiren de olsa, IM tanısı koyamamak yıkıcı sonuçlara yol açabilir. Radyologların ve cerrahların erişkin IM tanısı ve eşlik eden varyasyonlar hakkında bilgilendirilmesi önemlidir. IM genellikle bir vaka raporu olarak bildirildiğinden, eşlik eden varyasyonların sıklığını not etmek önemlidir. İntestinal malrotasyonun radyolojik bulgularını sunmak, erişkin intestinal malrotasyona eşlik eden abdominal varyasyonlara ve patolojilere farkındalığı artırmak ve tanı başarısızlığını azaltmak amaçlanmaktadır.
Yöntemler: Bilgisayarlı tomografi çekilen ve intestinal malrotasyon tanısı alan 18 yaş üzerindeki 32 olgunun BT’leri retrospektif olarak değerlendirildi. Pankreasta unsinat proses aplazisi veya hipoplazisi, psödomass şüphesi uyandırabilecek fokal kalınlaşma alanları, süperior mezenterik venin süperior mezenterik artere göre konumu, çekumun lokalizasyonu, sigmoid kolon redunsansisinin sıklığı belirlenecektir.
Bulgular: Bilgisayarlı tomografi çekilen erişkinlerde intestinal malrotasyon sıklığı 1/5375’tir. 32 olgunun 2’sinde akut batın nedeni saptanmış olup diğer olgular insidental olarak saptanmıştır. Pankreas unsinat proses aplazi veya hipoplazisi 21(%65,6) olguda ve sigmoid kolon redunsansisi 23 (%71,9) olguda rastlandı. Normal konumda çekum 8 (%25) olguda ve normal superior mesenterik arter-ven ilişkisi 6 (%18,8) olguda saptandı.
Sonuç: Erişkin intesitnal malrotasyona nadir olarak rastlanmaktadır. Karşılaşılan olguların büyük kısmına insidental olarak rastlanmaktadır. Erişkin intesitnal malrotasyona sıklıkla pankreas unsinat proses aplazi veya hipoplazisi eşlik etmektedir. Normal superior mesenterik arter-ven ilişkisi ve normal konumda çekum 4-5 olguda bir görülmektedir.

Anahtar Kelimeler

• İntestinal malrotasyon
• Bilgisayarlı tomografi
• Redundan kolon
• Unsinat proses

Visceral variations in adult intestinal malrotation: A case-series study

Abstract

Aim: Intestinal malrotation (IM) is a very rare rotational anomaly of midgut. Although uncommon, failure to diagnose IM may lead to devastating consequences. It is important that radiologists and surgeons are made aware of the diagnosis of adult IM and accompanying variations. Since IM is usually reported as a case report, it is important to note the frequency of the accompanying variations. It is aimed to present radiological findings of intestinal malrotation, increase awareness of abdominal variations and pathologies accompanying adult IM and reduce diagnostic failure.
Methods: Thirty-two patients aged over 18 years, who underwent computed tomography (CT) and received a diagnosis of IM, were retrospectively evaluated in terms of CT findings. Aplasia or hypoplasia of the uncinate process of the pancreas, focal thickening areas that may cause suspicion of a pseudomass, location of the superior mesenteric vein relative to the superior mesenteric artery, localization of the cecum, and the frequency of a redundant sigmoid colon were determined.
Results: The frequency of IM in adults undergoing CT was 1/5,375. In two of 32 cases, the cause of acute abdomen was identified while the other cases were detected incidentally. Aplasia or hypoplasia of the uncinate process of the pancreas and a redundant sigmoid colon were detected in 21 (65.6%) and 23 (71.9%) cases, respectively. The cecum was in the normal location in eight patients (25%), and there was a normal superior mesenteric artery-vein relationship in six (18.8%).
Conclusion: Intestinal malrotation is rarely encountered in adults and most cases are incidentally detected. IM is often accompanied by aplasia or hypoplasia of the uncinate process of the pancreas. A normal superior mesenteric artery-vein relationship and the cecum in the normal position are seen in one out of every four to five cases.

Keywords

• Intestinal malrotation
• Computed tomography
• Redundant colon
• Uncinate process

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