Koroner Arter Baypas Greft Operasyonu Geçiren Bartter Sendromlu Hastada Anestezi Yönetimi

Abstract

Frederic Bartter tarafından ilk kez 1962 yılında tanımlanan Bartter sendromu hipokalemi, metabolik alkaloz, hiperaldesteronizm, normal kan basıncı ve juxta glomerüler apparatusta hiperplazi ile karakterize nadir görülen kalıtsal bir hastalıktır. Özellikle açık kalp ameliyatı geçirecek bu hastalarda, asit-baz bozukluğu, elektrolit imbalansı, intravasküler volüm açığı, vazopressör ilaçlara karşı vasküler duyarsızlık ve trombosit agregasyonunda defekt gibi bu sendroma ait komplikasyonlar nedeniyle anestezi yönetimi açısından dikkat gerektirmektedir. Bu olgu sunumunda koroner arter baypas greft operasyonu uygulanan Bartter sendromlu hastada anestezi yönetimi sunuldu.

Keywords

• Bartter sendromu,koroner arter baypas greft,anestezi yönetimi

Anesthesia Management for Coronary Artery Bypass Grafting in a Patient with Bartter Syndrome

Abstract

Bartter syndrome, first described by Frederic Bartter in 1962, is a rare hereditary disease characterized by hypokalemia, metabolic alkalosis, hyperaldesteronism, normal blood pressure and hyperplasia of the juxtaglomerular apparatus. Complications of Bartter syndrome should be considered during anesthesia management in patients undergoing open heart surgery, including acid-base disorders, electrolyte imbalance, intravascular volume deficit, vascular insensitivity to vasopressor drugs and a defect in platelet aggregation. This case report discusses difficulties and challenges in anesthesia management of a patient with Bartter syndrome who underwent coronary artery by-pass grafting.

Keywords

• Bartter syndrome,coronary artery bypass grafting,anesthesia management

References

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