Different Faces of Cathecolaminergic Polymorphic Ventricular Tachycardia on Epinephrine QT Stress Testing

Abstract

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited arrhythmic disorder characterized by exercise-induced ventricular arrhythmias and risk for sudden cardiac death. An exercise stress test is a standard method for diagnosis of CPVT, characterized by typical bidirectional polymorphic ventricular tachycardia. In patients who are not suitable for an exercise stress test, epinephrine stress testing (epinephrine challenge) can be used instead. There are a few reports in the literature discussing supraventricular tachycardias during exercise testing in pediatric CPVT patients. We present a 6-year-old boy who was admitted with syncopy. Epinehrine stress testing was performed according to the Ackerman protocol and revealed different types of tachycardias.

Keywords

• Catecholaminergic polymorphic ventricular tachycardia
• epinehrine stress test
• supraventricular tachycardia

Adrenalin Stres Testi Sırasında Ortaya Çıkan Katekolaminerjik Polimorfik Ventriküler Taşikardinin Farklı Yüzleri

Abstract

Katekolaminerjik polimorfik ventriküler taşikardi (CPVT), egzersize bağlı ventriküler aritmi ve ani kardiyak ölüm riski ile karakterize kalıtımsal bir aritmik hastalıktır. Egzersiz stres testi, tipik çift yönlü polimorfik ventriküler taşikardilerle sonuçlanan CPVT tanısında standart bir yöntemdir. Egzersiz stres testi için uygun olmayan hastalarda, adrenalin stres testi kullanılabilir. Literatürde pediatrik CPVT hastalarında egzersiz testi sırasında supraventriküler taşikardilerle ilgili az sayıda rapor vardır. Bu olgu sunumunda senkop şikayeti ile başvuran altı yaşında erkek çocuk hastada Ackerman protokolüne göre uygulanan adrenalin stres testiyle ortaya çıkan farklı taşikardi türlerini paylaştık.

Keywords

• Adrenalin stres testi
• katekolaminerjik polimorfik ventriküler taşikardi
• supraventriküler taşikardi

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