End-Stage Hypertrophic Cardiomyopathy with Impressive Biventricular Hypertrophy: Evaluation with Novel Echocardiographic Modalities

Abstract

Hypertrophic cardiomyopathy is the most common genetic cardiac disorder. This disease, which is the leading cause of sudden cardiac death in young patients, is typically characterized by idiopathic hypertrophy of the left and sometimes the right ventricle. We present a case of end-stage hypertrophic cardiomyopathy with impressive biventricular hypertrophy which was evaluated with novel echocardiographic modalities.

Keywords

• Hypertrophic cardiomyopathy, impressive hypertrophy; imaging

Belirgin Biventriküler Hipertrofi Gösteren Son Dönem Hipertrofik Kardiyomiyopati Olgusu: Yeni Ekokardiyografik Yöntemlerle Değerlendirme

Abstract

Hipertrofik kardiyomiyopati en sık rastlanan genetik kökenli kalp hastalığıdır. Gençlerde gözlenen ani kardiyak ölümün en sık sebebi olan bu hastalıkta tipik olarak sol, bazen de sağ ventrikülün idiyopatik hipertrofisi gözlenmektedir. Bu çalışmada, belirgin biventriküler hipertrofi bulguları gösteren son dönem hipertrofik kardiyomiyopatili bir olgu yeni ekokardiyografik modaliteler ile incelenmiştir.

Keywords

• Hipertrofik kardiyomiyopati, belirgin hipertrofi; görüntüleme

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