Bidirectional Cavopulmonary (Glenn) Anastomosis in Pulmonary Atresia with Intact Ventricular Septum and Right Ventricle Dependent Coronary Circulation

Abstract

This is a case report of an 8-month-old infant with congenital heart disease including; pulmonary atresia, intact ventricular septum, right ventricular hypoplasia, atrial septal defect, coronary sinusoids (fistulas between right ventricle and left anterior descending artery). The patient had a stent for patent ductus arteriosus at 3 months of age and after 4 months a bidirectional Glenn shunt operation was performed with successful haemodynamics postoperatively.

Keywords

• Pulmonary atresia, intact ventricular septum, right ventricular dependent coronary circulation

Ventriküler Septumu ‹ntakt Pulmoner Atrezili Olguda Sa¤ Ventriküle Ba¤›ml› Koroner Sirkülasyonda Bidireksiyonel Kavopulmoner (Glenn) fiant Ameliyat›

Abstract

8 ayl›k sa¤ ventrikül hipoplazili, pulmoner atrezili, intak ventriküler septumlu, koroner sinosoidlerin sol anterior desenden arteri besledi¤i olguda patent duktus arteriozusun 3 ayl›k iken stent ile aç›lmas›ndan 4 ay sonra baflar›l› bidireksiyonel kavapulmoner (Glenn) flant ameliyat›, baflar›l› hemodinamik sonuçlarla yap›ld›.

Keywords

• Pulmoner atrezi, intak ventriküler septum, sa¤ ventriküle ba¤›ml› koroner sirkülasyon

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10. Bidirectional Cavapulmonary (Glenn) Anastomosis in ... 23 Kofluyolu Heart Journal