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Arrhythmogenic Right Ventricular Dysplasia Associated with Bicuspid Aortic Valve

Year 2010, Volume: 13 Issue: 2, 19 - 20, 01.02.2009

Ramazan Karg›n Mustafa Akcakoyun Soe Mao Aung Nihal Ozdemir Yunus Emiroglu

Abstract

A 22-year old boy was diagnosed arrhythmogenic right ventricular dysplasia (ARVD) with bicuspid aortic valve (BAV) after a symptomatic event of ventricular tachycardia originating from the right ventricle. Cardiac magnetic resonance imaging disclosed right ventricular enlargement, diffuse thinning of lateral wall and normal left ventricle. Echocardiography showed globally thinned, moderately enlarged right ventricle and bicuspid aortic valve. Cardiovascular malformations may be present with bicuspid aortic valve. Here we would like to report the first ARVD case with an accompanying BAV.

Keywords

Arrhythmogenic Right Ventricular Dysplasia Bicuspid Aortic Valve.

References

  • Marcus FI, Fontaine GH, Guiraudon G, Frank R, Laurenceau JL, Malergue C, et al. Right ventricular dysplasia: a report of 24 adult cases. Circulation; 1982; 65: 384–98.
  • Sen-Chowdhry S, Prasad SK, Syrris P, Wage R, Ward D, Mer- rifield R, et al. Cardiovascular magnetic resonance in arrhy- thmogenic right ventricular cardiomyopathy revisited: compari- son with task force criteria and genotype. J Am Coll Cardiol; 2006; 48: 2132-40.
  • Ainsworth CD, Skanes AC, Klein GJ, Gula LJ, Yee R, Krahn AD. Differentiating arrhythmogenic right ventricular cardiom- yopathy from right ventricular outflow tract ventricular tach- ycardia using multilead QRS duration and axis. Heart Rhythm; 2006; 4:416-23
  • Hoffman JI, Kaplan S. The incidence of congenital heart di- sease. J Am Coll Cardiol; 2002; 39: 1890–900.
  • Gershoni-Baruch R, Moor EV, Enat R. Marfan syndrome as- sociated with bicuspid aortic valve, premature aging, and pri- mary hypogonadism. Am J Med Genet; 1990; 37: 169–72.
  • Hirose H, Amano A, Takahashi A, Nagano N, Kohmoto T. Ruptured aortic dissecting aneurysm in Turner's syndrome: a case report and review of literature. Ann Thorac Cardiovasc Surg; 2000; 6: 275–80. normal left ventricular function.

Aritmojenik Sa¤ Ventrikül Displazisi ile Birlikte Olan Biküspit Aort Kapak

Year 2010, Volume: 13 Issue: 2, 19 - 20, 01.02.2009

Ramazan Karg›n Mustafa Akcakoyun Soe Mao Aung Nihal Ozdemir Yunus Emiroglu

Abstract

Sa¤ ventrikül kaynakl› ventriküler taflikardiye ba¤l› semptomu olan 22 yafl›nda erkek bir hastada aritmojenik sa¤ ventrikül displaziye (ASVD) efllik eden bikuspit aortik kapak (BAK) saptad›k. Kardiyak manyetik rezonans görüntülemede sa¤ ventrikül lateral duvarda yayg›n incelme ile geniflleme ve normal sol ventrikül saptand›. Ekokardiyografide ise sa¤ ventrikülde orta derece geniflleme ile global incelme ve BAK saptad›k. Bikuspit aortik kapak di- ¤er kardiyovasküler malformasyon ile birlikte bulunabilmektedir. Biz bu yaz›m›zda ilk defa ASVD'ye efllik eden BAK olgusunu bildirdik.

Keywords

Aritmojenik Sa¤ Ventrikül Displazisi Bikuspit Aortik Kapak

References

  • Marcus FI, Fontaine GH, Guiraudon G, Frank R, Laurenceau JL, Malergue C, et al. Right ventricular dysplasia: a report of 24 adult cases. Circulation; 1982; 65: 384–98.
  • Sen-Chowdhry S, Prasad SK, Syrris P, Wage R, Ward D, Mer- rifield R, et al. Cardiovascular magnetic resonance in arrhy- thmogenic right ventricular cardiomyopathy revisited: compari- son with task force criteria and genotype. J Am Coll Cardiol; 2006; 48: 2132-40.
  • Ainsworth CD, Skanes AC, Klein GJ, Gula LJ, Yee R, Krahn AD. Differentiating arrhythmogenic right ventricular cardiom- yopathy from right ventricular outflow tract ventricular tach- ycardia using multilead QRS duration and axis. Heart Rhythm; 2006; 4:416-23
  • Hoffman JI, Kaplan S. The incidence of congenital heart di- sease. J Am Coll Cardiol; 2002; 39: 1890–900.
  • Gershoni-Baruch R, Moor EV, Enat R. Marfan syndrome as- sociated with bicuspid aortic valve, premature aging, and pri- mary hypogonadism. Am J Med Genet; 1990; 37: 169–72.
  • Hirose H, Amano A, Takahashi A, Nagano N, Kohmoto T. Ruptured aortic dissecting aneurysm in Turner's syndrome: a case report and review of literature. Ann Thorac Cardiovasc Surg; 2000; 6: 275–80. normal left ventricular function.
There are 6 citations in total.

Details

Primary Language Turkish
Journal Section Articles
Authors

Ramazan Karg›n This is me

Mustafa Akcakoyun This is me

Soe Mao Aung This is me

Nihal Ozdemir This is me

Yunus Emiroglu This is me

Publication Date February 1, 2009
Published in Issue Year 2010 Volume: 13 Issue: 2

Cite

APA Karg›n, R. ., Akcakoyun, M. ., Aung, S. M. ., Ozdemir, N. ., et al. (2009). Aritmojenik Sa¤ Ventrikül Displazisi ile Birlikte Olan Biküspit Aort Kapak. Koşuyolu Kalp Dergisi, 13(2), 19-20. https://doi.org/10.17557/tjfc.18686
AMA Karg›n R, Akcakoyun M, Aung SM, Ozdemir N, Emiroglu Y. Aritmojenik Sa¤ Ventrikül Displazisi ile Birlikte Olan Biküspit Aort Kapak. Koşuyolu Kalp Dergisi. February 2009;13(2):19-20. doi:10.17557/tjfc.18686
Chicago Karg›n, Ramazan, Mustafa Akcakoyun, Soe Mao Aung, Nihal Ozdemir, and Yunus Emiroglu. “Aritmojenik Sa¤ Ventrikül Displazisi Ile Birlikte Olan Biküspit Aort Kapak”. Koşuyolu Kalp Dergisi 13, no. 2 (February 2009): 19-20. https://doi.org/10.17557/tjfc.18686.
EndNote Karg›n R, Akcakoyun M, Aung SM, Ozdemir N, Emiroglu Y (February 1, 2009) Aritmojenik Sa¤ Ventrikül Displazisi ile Birlikte Olan Biküspit Aort Kapak. Koşuyolu Kalp Dergisi 13 2 19–20.
IEEE R. . Karg›n, M. . Akcakoyun, S. M. . Aung, N. . Ozdemir, and Y. . Emiroglu, “Aritmojenik Sa¤ Ventrikül Displazisi ile Birlikte Olan Biküspit Aort Kapak”, Koşuyolu Kalp Dergisi, vol. 13, no. 2, pp. 19–20, 2009, doi: 10.17557/tjfc.18686.
ISNAD Karg›n, Ramazan et al. “Aritmojenik Sa¤ Ventrikül Displazisi Ile Birlikte Olan Biküspit Aort Kapak”. Koşuyolu Kalp Dergisi 13/2 (February 2009), 19-20. https://doi.org/10.17557/tjfc.18686.
JAMA Karg›n R, Akcakoyun M, Aung SM, Ozdemir N, Emiroglu Y. Aritmojenik Sa¤ Ventrikül Displazisi ile Birlikte Olan Biküspit Aort Kapak. Koşuyolu Kalp Dergisi. 2009;13:19–20.
MLA Karg›n, Ramazan et al. “Aritmojenik Sa¤ Ventrikül Displazisi Ile Birlikte Olan Biküspit Aort Kapak”. Koşuyolu Kalp Dergisi, vol. 13, no. 2, 2009, pp. 19-20, doi:10.17557/tjfc.18686.
Vancouver Karg›n R, Akcakoyun M, Aung SM, Ozdemir N, Emiroglu Y. Aritmojenik Sa¤ Ventrikül Displazisi ile Birlikte Olan Biküspit Aort Kapak. Koşuyolu Kalp Dergisi. 2009;13(2):19-20.