İnfantil Myofibrom: Olgu Sunumu

Year 2019, Volume: 11 Issue: 3, 81 - 84, 30.12.2019

Zeynep Betül Erdem , Özben Yalçın Ayşe Tülay Sayılgan

Abstract

Özet: İnfantil miyofibrom(IM), miyofibroblastların benign proliferasyonu ile karakterize mezenkimal bir bozukluktur. Genel popülasyonda nadir görülse de, çocukluk çağının en sık görülen fibroblastik tümörüdür (%20-%25). Üç tipi tanımlanmıştır: soliter IM, visseral tutulum olmaksızın multisentrik IM, visseral tutulumun görüldüğü IM. Morfolojik özellikler her üç formda da aynıdır fakat visseral tutulumun görüldüğü formda morbidite ve mortalite oranı yüksektir, prognoz kötüdür. Nadir rastlanan ve maligniteler ile karışabilen bu antiteyi, bir olgu ve literatür bilgileri eşliğinde sunduk.
Abstract: Infantile myofibroma(IM) is a mesenchymal disorder characterized by benign proliferation of myofibroblasts. Although rare, it is one of the most common fibroblastic tumors of the infancy and childhood. There are three forms defined: solitary IM, multicentric IM without visceral involment, and IM with visceral involvement. There are no histopathologic differences inbetween these forms but visceral involvement is associated with high morbidity and mortality. We report a rare case of infantile myofibroma which can be mistaken as malignancy.

Keywords

İnfantil myofibrom, yumuşak doku neoplazileri

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